POSTOPERATIVE METABOLIC DECOMPENSATION IN MAPLE-SYRUP-URINE-DISEASE IS COMPLETELY PREVENTED BY INSULIN

被引:3
作者
BIGGEMANN, B
ZASS, R
WENDEL, U
机构
[1] Universitäts-Kinderklinik, Heinrich-Heine Universität, Düsseldorf, D-40000
关键词
D O I
10.1007/BF00714298
中图分类号
R5 [内科学];
学科分类号
1002 ; 100201 ;
摘要
[No abstract available]
引用
收藏
页码:912 / 913
页数:2
相关论文
共 4 条
  • [1] BRANCHED-CHAIN AMINO-ACID FREE PARENTERAL-NUTRITION IN THE TREATMENT OF ACUTE METABOLIC DECOMPENSATION IN PATIENTS WITH MAPLE SYRUP URINE DISEASE
    BERRY, GT
    HEIDENREICH, R
    KAPLAN, P
    LEVINE, F
    MAZUR, A
    PALMIERI, MJ
    YUDKOFF, M
    SEGAL, S
    [J]. NEW ENGLAND JOURNAL OF MEDICINE, 1991, 324 (03) : 175 - 179
  • [2] EFFECT OF INSULIN AND PLASMA AMINO-ACID-CONCENTRATIONS ON LEUCINE METABOLISM IN MAN - ROLE OF SUBSTRATE AVAILABILITY ON ESTIMATES OF WHOLE-BODY PROTEIN-SYNTHESIS
    CASTELLINO, P
    LUZI, L
    SIMONSON, DC
    HAYMOND, M
    DEFRONZO, RA
    [J]. JOURNAL OF CLINICAL INVESTIGATION, 1987, 80 (06) : 1784 - 1793
  • [3] PHENYLALANINE LEVELS IN PKU FOLLOWING MINOR SURGERY
    FIEDLER, AE
    MILLER, MJ
    BICKEL, H
    CEDERBAUM, SD
    [J]. AMERICAN JOURNAL OF MEDICAL GENETICS, 1982, 11 (04): : 411 - 414
  • [4] DOSE-RESPONSE CURVES OF EFFECTS OF INSULIN ON LEUCINE KINETICS IN HUMANS
    TESSARI, P
    TREVISAN, R
    INCHIOSTRO, S
    BIOLO, G
    NOSADINI, R
    DEKREUTZENBERG, SV
    DUNER, E
    TIENGO, A
    CREPALDI, G
    [J]. AMERICAN JOURNAL OF PHYSIOLOGY, 1986, 251 (03): : E334 - E342