PFAPA syndrome

被引：7

作者：

Andre, Suzete ^{[1
]}

Vales, Fernando ^{[1
]}

Cardoso, Eduardo ^{[1
]}

Santos, Margarida ^{[1
]}

机构：

[1] Hosp Sao Joao, Serv Otorrinolaringol, Oporto, Portugal

来源：

ACTA OTORRINOLARINGOLOGICA ESPANOLA | 2009年 / 60卷 / 03期

关键词：

PFAPA syndrome; Periodic fever; Corticoid therapy; Tonsillectomy;

D O I：

10.1016/S0001-6519(09)71233-6

中图分类号：

R76 [耳鼻咽喉科学];

学科分类号：

100213 ;

摘要：

PFAPA syndrome is characterized by periodic fever, pharyngitis, cervical adenitis and aphthous stomatitis. The bouts of fever can last for days or even weeks. Between crises, patients remain asymptomatic for variable periods. It appears before the age of fi ve and has limited duration (4-8 years). Its aetiopathogeny is unknown. Corticoids are the treatment of choice. Tonsillectomy has been proposed as a solution but remains controversial. We present the case of a 4-year-old girl with PFAPA syndrome who underwent tonsillectomy in January, 2008, and we review the literature. (C) 2008 Elsevier Espana, S.L. All rights reserved.

引用

页码：208 / 209

页数：2

共 50 条

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[49] Tonsillectomy efficacy in children with PFAPA syndrome is comparable to the standard medical treatment: a long-term observational study [J].

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