PFAPA syndrome

被引:7
作者
Andre, Suzete [1 ]
Vales, Fernando [1 ]
Cardoso, Eduardo [1 ]
Santos, Margarida [1 ]
机构
[1] Hosp Sao Joao, Serv Otorrinolaringol, Oporto, Portugal
来源
ACTA OTORRINOLARINGOLOGICA ESPANOLA | 2009年 / 60卷 / 03期
关键词
PFAPA syndrome; Periodic fever; Corticoid therapy; Tonsillectomy;
D O I
10.1016/S0001-6519(09)71233-6
中图分类号
R76 [耳鼻咽喉科学];
学科分类号
100213 ;
摘要
PFAPA syndrome is characterized by periodic fever, pharyngitis, cervical adenitis and aphthous stomatitis. The bouts of fever can last for days or even weeks. Between crises, patients remain asymptomatic for variable periods. It appears before the age of fi ve and has limited duration (4-8 years). Its aetiopathogeny is unknown. Corticoids are the treatment of choice. Tonsillectomy has been proposed as a solution but remains controversial. We present the case of a 4-year-old girl with PFAPA syndrome who underwent tonsillectomy in January, 2008, and we review the literature. (C) 2008 Elsevier Espana, S.L. All rights reserved.
引用
收藏
页码:208 / 209
页数:2
相关论文
共 50 条
[21]   Diagnosis of PFAPA syndrome applied to a cohort of 17 adults with unexplained recurrent fevers [J].
Cantarini, L. ;
Vitale, A. ;
Bartolomei, B. ;
Galeazzi, M. ;
Rigante, D. .
CLINICAL AND EXPERIMENTAL RHEUMATOLOGY, 2012, 30 (02) :269-271
[22]   The clinical characteristics of PFAPA syndrome [J].
Sara Sebnem Kilic .
Pediatric Rheumatology, 12 (Suppl 1)
[23]   Periodic fever, aphthous stomatitis, pharyngitis and cervical adenitis (PFAPA syndrome) in adults [J].
Onderka, C. E. ;
Ridder, G. J. .
DEUTSCHE MEDIZINISCHE WOCHENSCHRIFT, 2012, 137 (10) :471-475
[24]   Vestibular involvement of PFAPA syndrome [J].
Kuzu, Selcuk ;
Gunebakan, Caglar ;
Yildiz, Erkan ;
Kahveci, Orhan Kemal ;
Bucak, Abdulkadir .
AMERICAN JOURNAL OF OTOLARYNGOLOGY, 2021, 42 (03)
[25]   PFAPA syndrome: Diagnosis in adulthood [J].
Hernandez Vidal, M. J. ;
Trasancos Escura, C. ;
Meseguer Noguera, R. ;
Gil Ortega, M. del M. .
REVISTA CLINICA ESPANOLA, 2015, 215 (03) :192-193
[26]   Evaluation of Clinical and Laboratory Characteristics of Patients with PFAPA Syndrome [J].
Gungorer, Vildan ;
Yorulmaz, Alaaddin ;
Arslan, Sukru .
GUNCEL PEDIATRI-JOURNAL OF CURRENT PEDIATRICS, 2020, 18 (03) :444-456
[27]   PFAPA syndrome is not a sporadic disease [J].
Cochard, Marie ;
Clet, Johanna ;
Le, Lan ;
Pillet, Pascal ;
Onrubia, Xavier ;
Gueron, Thierry ;
Faouzi, Mohammed ;
Hofer, Michael .
RHEUMATOLOGY, 2010, 49 (10) :1984-1987
[28]   Demographic, clinical and therapeutic findings in a monocentric cohort of adult patients with suspected PFAPA syndrome [J].
Vitale, A. ;
Orlando, I. ;
Lopalco, G. ;
Emmi, G. ;
Cattalini, M. ;
Frediani, B. ;
Galeazzi, M. ;
Iannone, F. ;
Rigante, D. ;
Cantarini, L. .
CLINICAL AND EXPERIMENTAL RHEUMATOLOGY, 2016, 34 (06) :S77-S81
[29]   Benefits and Importance of Tonsillectomy in Children and Youth with PFAPA Syndrome [J].
Ridder, G. J. ;
Onderka, C. E. .
LARYNGO-RHINO-OTOLOGIE, 2011, 90 (10) :609-616
[30]   Mumps, measles and rubella vaccination in children with PFAPA syndrome [J].
Kraszewska-Glomba, Barbara ;
Matkowska-Kocjan, Agnieszka ;
Miskiewicz, Katarzyna ;
Szymanska-Toczek, Zofia ;
Wojcik, Marta ;
Banys, Dorota ;
Szenborn, Leszek .
VACCINE, 2016, 34 (48) :5903-5906