Urticaria pigmentosa is one of a spectrum of diseases of the mast cell, termed mastocytosis. This is an uncommon disorder inwhich mast cells are overproduced and accumulate in various organs. In urticaria pigmentosa, mast cells accumulate in the skin, causing a rash. In this article, the diagnosis and management of urticaria pigmentosa will be reviewed by examining a case occurring in a 5-month-old boy. There is also a brief review of systemicmastocytosis and other mastocytosis variants.
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Univ Life Sci Lublin, Fac Vet Med, Subdept Clin Diagnost & Vet Dermatol, Lublin, PolandUniv Life Sci Lublin, Fac Vet Med, Subdept Clin Diagnost & Vet Dermatol, Lublin, Poland
Szczepanik, Marcin
Wilkolek, Piotr
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Univ Life Sci Lublin, Fac Vet Med, Subdept Clin Diagnost & Vet Dermatol, Lublin, PolandUniv Life Sci Lublin, Fac Vet Med, Subdept Clin Diagnost & Vet Dermatol, Lublin, Poland
Wilkolek, Piotr
Kalisz, Grzegorz
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Med Univ Lublin, Fac Pharm, Dept Biopharm, Ul W Chodzki 4a, Lublin, PolandUniv Life Sci Lublin, Fac Vet Med, Subdept Clin Diagnost & Vet Dermatol, Lublin, Poland
Kalisz, Grzegorz
Smiech, Anna
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Univ Life Sci Lublin, Dept Pathol, Gleboka 30, PL-20620 Lublin, PolandUniv Life Sci Lublin, Fac Vet Med, Subdept Clin Diagnost & Vet Dermatol, Lublin, Poland
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Nihon Univ, Grad Sch Med Sci, Adv Med Res Ctr, Div Mol Cell Immunol & Allergol, Tokyo, JapanKyoto Univ Hosp, Dept Diagnost Pathol, Kyoto 6068507, Japan