PACHYDERMODACTYLY AND ATROPHIA MACULOSA VARIOLIFORMIS CUTIS

被引:23
作者
CALLOT, V
WECHSLER, J
HOVNANIAN, A
REVUZ, J
机构
[1] HOP HENRI MONDOR,DEPT DERMATOL,F-94010 CRETEIL,FRANCE
[2] HOP HENRI MONDOR,DEPT PATHOL,F-94010 CRETEIL,FRANCE
关键词
PACHYDERMODACTYLY; KNUCKLE PADS; DIGITAL FIBROMATOSIS; ATROPHIA MACULOSA VARIOLIFORMIS CUTIS;
D O I
10.1159/000246636
中图分类号
R75 [皮肤病学与性病学];
学科分类号
100206 ;
摘要
Pachydermodactyly is a rare form of superficial digital fibromatosis characterized by progressive asymptomatic thickening of the back and sides of the proximal interphalangeal joints of the fingers. Atrophia maculosa varioliformis cutis is an acquired dermal atrophy, localized on the cheeks. Only a few cases of each pathology have been published. We find it interesting to report the case of a patient with both conditions as these two connective-tissue diseases are very rare. The association is probably fortuitous.
引用
收藏
页码:56 / 58
页数:3
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