DIRECT DEMONSTRATION THAT THE DEFICIENT OXIDATION OF VERY LONG-CHAIN FATTY-ACIDS IN X-LINKED ADRENOLEUKODYSTROPHY IS DUE TO AN IMPAIRED ABILITY OF PEROXISOMES TO ACTIVATE VERY LONG-CHAIN FATTY-ACIDS

被引：149
作者：
WANDERS, RJA
VANROERMUND, CWT
VANWIJLAND, MJA
SCHUTGENS, RBH
VANDENBOSCH, H
SCHRAM, AW
TAGER, JM
机构：
[1] STATE UNIV UTRECHT,BIOCHEM LAB,3584 CH UTRECHT,NETHERLANDS
[2] UNIV AMSTERDAM,BIOCHEM LAB,1000 HD AMSTERDAM,NETHERLANDS
来源：
BIOCHEMICAL AND BIOPHYSICAL RESEARCH COMMUNICATIONS | 1988年 / 153卷 / 02期
关键词：
D O I：
10.1016/S0006-291X(88)81140-9
中图分类号：
Q5 [生物化学]; Q7 [分子生物学];
学科分类号：
071010 ; 081704 ;
摘要：
引用
收藏
页码：618 / 624
页数：7
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