Improved pulmonary function following pirfenidone treatment in a patient with progressive interstitial lung disease associated with systemic sclerosis

被引：37

作者：

Udwadia, Zarir F. ^{[1
]}

Mullerpattan, Jai B. ^{[1
]}

Balakrishnan, Canchi ^{[2
]}

Richeldi, Luca ^{[3
]}

机构：

[1] PD Hinduja Natl Hosp & Med Res Ctr, Dept Resp Med, Veer Savarkar Marg, Bombay 400016, Maharashtra, India

[2] PD Hinduja Natl Hosp & Med Res Ctr, Dept Rheumatol, Bombay, Maharashtra, India

[3] Univ Modena & Reggio Emilia, Dept Resp Med, Ctr Rare Lung Dis, Chair Interstitial Lung Dis, Modena, Italy

来源：

LUNG INDIA | 2015年 / 32卷 / 01期

关键词：

Interstitial lung disease; pirfenidone; systemic sclerosis;

D O I：

10.4103/0970-2113.148451

中图分类号：

R56 [呼吸系及胸部疾病];

学科分类号：

摘要：

Pirfenidone is an anti-fibrotic drug which has been approved for the management of patients with Idiopathic Pulmonary Fibrosis (IPF). However, its role in interstitial lung disease (ILD) due to other causes such as systemic sclerosis (SSc) is not clear. We present a case of a patient with SSc associated ILD who showed a subjective as well as objective improvement in lung function with pirfenidone.

引用

页码：50 / 52

页数：3

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