A case of Hirschsprung's disease underwent surgery in adulthood

被引：3

作者：

Nakatake, Richi ^{[1
]}

Hamada, Yoshinori ^{[1
]}

Miki, Hirokazu ^{[1
]}

Shirai, Takeshi ^{[1
]}

Nakamura, Yusuke ^{[1
]}

Hamada, Hiroshi ^{[1
]}

Ishizaki, Morihiko ^{[1
]}

Kon, Masanori ^{[2
]}

机构：

[1] Kansai Med Univ, Dept Surg, Div Pediat Surg, 2-5-1 Hirakata, Hirakata, Osaka 5731191, Japan

[2] Kansai Med Univ, Dept Surg, 2-5-1 Hirakata, Hirakata, Osaka 5731191, Japan

来源：

JOURNAL OF PEDIATRIC SURGERY CASE REPORTS | 2016年 / 13卷

关键词：

Hirschsprung's disease; Adult case; Duhamel-GIA procedure;

D O I：

10.1016/j.epsc.2016.07.005

中图分类号：

R72 [儿科学];

学科分类号：

100202 ;

摘要：

Adult Hirschsprung's disease is a rare motor disorder of the gut that is frequently misdiagnosed as refractory constipation. We describe a 30-year-old patient with adult Hirschsprung's disease with a history of chronic constipation requiring daily enema. Barium enema and rectal biopsy showed short segment-type Hirschsprung's disease with a grossly distended sigmoid colon with fecal retention. Staged operations, including the Duhamel-GIA method as a definitive surgery, completely resolved the patient's symptoms. There were no complications by the end of a 7-year follow-up. Adult Hirschsprung's disease should be considered in the differential diagnosis of cases where adult patients present with chronic constipation. Despite technical difficulty of the modified Duhamel-GIA procedure due to chronic fibrous changes of the rectum, it is a feasible surgical option for treating cases of adult Hirschsprung's disease. (C) 2016 The Authors. Published by Elsevier Inc.

引用

页码：1 / 5

页数：5

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