Obstructed hemivagina with ipsilateral renal agenesis (OHVIRA) syndrome with imperforate anus

被引：0

作者：

Cosgrove, Peter ^{[1
]}

Kahlden, Kyle ^{[1
]}

Barr, Lori ^{[2
]}

Sanchez, Julie ^{[3
]}

机构：

[1] Dell Childrens Med Ctr, Dept Pediat, Pediat Residency Program, 4900 Mueller Blvd, Austin, TX 78723 USA

[2] Dell Childrens Med Ctr, Dept Radiol, 4900 Mueller Blvd, Austin, TX 78723 USA

[3] Dell Childrens Med Ctr, Dept Pediat Surg, 4900 Mueller Blvd, Austin, TX 78723 USA

来源：

JOURNAL OF PEDIATRIC SURGERY CASE REPORTS | 2016年 / 12卷

关键词：

OHVIRA; Uterine didelphys; Anorectal malformation;

D O I：

10.1016/j.epsc.2016.06.015

中图分类号：

R72 [儿科学];

学科分类号：

100202 ;

摘要：

OHVIRA syndrome (Obstructed hemivagina with ipsilateral renal agenesis) is a rare Mullerian duct anomaly that results in uterine didelphys, obstructed vaginal vault, and unilateral renal agenesis. We report an 11 year old girl with a history of imperforate anus presenting with progressive abdominal pain. This represents the first documented case of OHVIRA syndrome in association with an ano-rectal malformation. (C) 2016 The Authors. Published by Elsevier Inc. This is an open access article under the CC BY-NC-ND license

引用

页码：34 / 37

页数：4

共 33 条

[31] Three-Dimensional Technology to Diagnose Unilateral Cervical Atresia in Obstructive Hemivagina with Ipsilateral Renal Anomaly: A Case Report and Review of the Literature
Tomlin, Kristl
Barnes, Craig
Van Leeuwen, Kathy
Williamson, Amy
JOURNAL OF PEDIATRIC AND ADOLESCENT GYNECOLOGY, 2018, 31 (01) : 67 - 70
[32] A New Case of Herlyn-Werner-Wunderlich Syndrome: Uterine Didelphys with Unilateral Cervical Dysgenesis, Vaginal Agenesis, Cervical Distal Ureteral Remnant Fistula, Ureterocele, and Renal Agenesis in a Patient with Contralateral Multicystic Dysplastic Kidney
Yu, Jin-Hee
Lee, Sa-Ra
Choi, Heayeon
Kim, Kun-Suk
Kang, Byung-Moon
DIAGNOSTICS, 2022, 12 (01)
[33] Diverse ultrasound image features of unilateral genital tract obstruction with ipsilateral renal anomaly syndrome on genitourinary system segmental sequential ultrasound screening and the accuracy of ultrasonic diagnosis
Zhang, Ling
Liu, Rong
Liu, Ronghua
Wu, Mingfu
Ye, Shuangmei
QUANTITATIVE IMAGING IN MEDICINE AND SURGERY, 2023, 13 (10) : 7194 - 7213

← 1 2 3 4 →