Obstructed hemivagina with ipsilateral renal agenesis (OHVIRA) syndrome with imperforate anus

被引:0
作者
Cosgrove, Peter [1 ]
Kahlden, Kyle [1 ]
Barr, Lori [2 ]
Sanchez, Julie [3 ]
机构
[1] Dell Childrens Med Ctr, Dept Pediat, Pediat Residency Program, 4900 Mueller Blvd, Austin, TX 78723 USA
[2] Dell Childrens Med Ctr, Dept Radiol, 4900 Mueller Blvd, Austin, TX 78723 USA
[3] Dell Childrens Med Ctr, Dept Pediat Surg, 4900 Mueller Blvd, Austin, TX 78723 USA
关键词
OHVIRA; Uterine didelphys; Anorectal malformation;
D O I
10.1016/j.epsc.2016.06.015
中图分类号
R72 [儿科学];
学科分类号
100202 ;
摘要
OHVIRA syndrome (Obstructed hemivagina with ipsilateral renal agenesis) is a rare Mullerian duct anomaly that results in uterine didelphys, obstructed vaginal vault, and unilateral renal agenesis. We report an 11 year old girl with a history of imperforate anus presenting with progressive abdominal pain. This represents the first documented case of OHVIRA syndrome in association with an ano-rectal malformation. (C) 2016 The Authors. Published by Elsevier Inc. This is an open access article under the CC BY-NC-ND license
引用
收藏
页码:34 / 37
页数:4
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