SEZARYS SYNDROME - CLINICAL EVALUATION OF 8 PATIENTS

被引:18
作者
HAMMINGA, L [1 ]
HARTGRINKGROENEVELD, CA [1 ]
VANVLOTEN, WA [1 ]
机构
[1] STATE UNIV LEIDEN HOSP,DEPT HAEMATOL,LEIDEN,NETHERLANDS
关键词
D O I
10.1111/j.1365-2133.1979.tb06201.x
中图分类号
R75 [皮肤病学与性病学];
学科分类号
100206 ;
摘要
Clinical and laboratory investigations of 8 patients with Sézary's syndrome are presented. Sézary cells were found in peripheral blood as well as in bone marrow and lymph nodes. The overall follow‐up period was 8 years. Different therapeutic regimens were given. The best results were obtained with chlorambucil and prednisone orally, combined with topical application of nitrogen mustard. Three patients died of pneumonia and septicaemia. Copyright © 1979, Wiley Blackwell. All rights reserved
引用
收藏
页码:291 / 296
页数:6
相关论文
共 18 条
[1]  
BARRETT AJ, 1976, LANCET, V1, P940
[2]   SEZARYS SYNDROME - CYTOGENETIC, CYTOPHOTOMETRIC AND AUTORADIOGRAPHIC STUDY [J].
BOSMAN, FT ;
VANVLOTEN, WA .
JOURNAL OF PATHOLOGY, 1976, 118 (01) :49-+
[3]   SEZARY SYNDROME - MALIGNANT PROLIFERATION OF HELPER T CELLS [J].
BRODER, S ;
EDELSON, RL ;
LUTZNER, MA ;
NELSON, DL ;
MACDERMOTT, RP ;
DURM, ME ;
GOLDMAN, CK ;
MEADE, BD ;
WALDMANN, TA .
JOURNAL OF CLINICAL INVESTIGATION, 1976, 58 (06) :1297-1306
[4]   LEUKEMIC CELLS WITH MEMBRANE PROPERTIES OF THYMUS-DERIVED (T) LYMPHOCYTES IN A CASE OF SEZARYS SYNDROME - MORPHOLOGIC AND IMMUNOLOGICAL STUDIES [J].
BROOME, JD ;
ZUCKERFR.D ;
WEINER, MS ;
BIANCO, C ;
NUSSENZWEIG, V .
CLINICAL IMMUNOLOGY AND IMMUNOPATHOLOGY, 1973, 1 (03) :319-329
[5]   INDICATIONS OF THYMUS-DERIVED NATURE OF PROLIFERATING CELLS IN 6 PATIENTS WITH SEZARYS SYNDROME [J].
BROUET, JC ;
FLANDRIN, G ;
SELIGMANN, M .
NEW ENGLAND JOURNAL OF MEDICINE, 1973, 289 (07) :341-344
[6]   SUCCESSFUL MANAGEMENT OF SEZARY SYNDROME - MOBILIZATION AND REMOVAL OF EXTRAVASCULAR NEOPLASTIC-T CELLS BY LEUKAPHERESIS [J].
EDELSON, R ;
FACKTOR, M ;
ANDREWS, A ;
LUTZNER, M ;
SCHEIN, P .
NEW ENGLAND JOURNAL OF MEDICINE, 1974, 291 (06) :293-294
[7]   ULTRASTRUCTURE OF ABNORMAL CELLS IN SEZARY SYNDROME, MYCOSIS FUNGOIDES, AND PARAPSORIASIS EN PLAQUE [J].
LUTZNER, MA ;
HOBBS, JW ;
HORVATH, P .
ARCHIVES OF DERMATOLOGY, 1971, 103 (04) :375-+
[8]   CYTOGENETIC, CYTOPHOTOMETRIC, AND ULTRASTRUCTURAL STUDY OF LARGE CEREBRIFORM CELLS OF SEZARY SYNDROME AND DESCRIPTION OF A SMALL-CELL VARIANT [J].
LUTZNER, MA ;
EMERIT, I ;
DUREPAIR.R ;
FLANDRIN, G ;
GRUPPER, C ;
PRUNIERA.M .
JOURNAL OF THE NATIONAL CANCER INSTITUTE, 1973, 50 (05) :1145-1162
[9]  
MEYER CJLM, 1977, VIRCHOWS ARCH B, V25, P95
[10]  
ROSNER F, 1976, CANCER, V37, P1033, DOI 10.1002/1097-0142(197602)37:2+<1033::AID-CNCR2820370807>3.0.CO