GROWTH-HORMONE DEFICIENCY AND EMPTY SELLA IN DIDMOAD SYNDROME - AN ENDOCRINE STUDY

被引：22
|
作者：
SOLIMAN, AT
BAPPAL, B
DARWISH, A
RAJAB, A
ASFOUR, M
机构：
[1] ROYAL HOSP,DEPT ENDOCRINOL,MASQAT,OMAN
[2] ROYAL HOSP,DEPT RADIOL,MASQAT,OMAN
[3] ROYAL HOSP,DEPT PEDIAT,MASQAT,OMAN
来源：
ARCHIVES OF DISEASE IN CHILDHOOD | 1995年 / 73卷 / 03期
关键词：
DIDMOAD SYNDROME; GROWTH HORMONE; EMPTY SELLA; INSULIN;
D O I：
10.1136/adc.73.3.251
中图分类号：
R72 [儿科学];
学科分类号：
100202 ;
摘要：
Two girls with DIDMOAD syndrome are presented. One also had severe megaloblastic-sideroblastic anaemia and the other several neurological manifestations. Both were short with defective growth hormone secretion. Computed tomography revealed empty sella in both girls; one had widespread atrophic cortical and cerebellar changes. High doses of thiamine improved the anaemia in the first case increased C peptide secretion in both, but had no effect on the neurological abnormalities.
引用
收藏
页码：251 / 253
页数：3
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