DESMOPLASTIC SMALL-CELL TUMOR OF THE OVARY - A UNIQUE POLYPHENOTYPIC TUMOR WITH AN UNFAVORABLE PROGNOSIS

被引：30

作者：

ZALOUDEK, C ^{[1
]}

MILLER, TR ^{[1
]}

STERN, JL ^{[1
]}

机构：

[1] UNIV CALIF SAN FRANCISCO,DEPT OBSTET & GYNAECOL,DIV GYNECOL ONCOL,SAN FRANCISCO,CA 94143

来源：

INTERNATIONAL JOURNAL OF GYNECOLOGICAL PATHOLOGY | 1995年 / 14卷 / 03期

关键词：

OVARY; OVARIAN NEOPLASMS; DESMOPLASTIC SMALL CELL TUMOR; IMMUNOHISTOCHEMISTRY; FINE NEEDLE ASPIRATION;

D O I：

10.1097/00004347-199507000-00011

中图分类号：

R71 [妇产科学];

学科分类号：

100211 ;

摘要：

Desmoplastic small cell tumor (DSCT) is a recently described intraabdominal neoplasm of uncertain histogenesis that occurs predominantly in boys and young men. We report a case in a young woman that presented clinically as bilateral ovarian tumors with extensive pelvic and abdominal dissemination. The patient had cytoreductive surgery followed by combination chemotherapy. She had a complete clinical remission, but tumor recurrence was detected 1 year after diagnosis and the patient died of her disease 18 months after presentation. DSCT has a distinctive histologic appearance and a unique immunophenotype. It can present as an ovarian neoplasm and must be considered in the differential diagnosis of small cell tumors of the ovary.

引用

页码：260 / 265

页数：6