SOME PROPERTIES OF CERULOPLASMIN FROM PATIENTS WITH WILSONS DISEASE

被引:14
作者
CARRICO, RJ
DEUTSCH, HF
机构
[1] Department of Physiological Chemistry, University of Wisconsin, Madison
来源
BIOCHEMICAL MEDICINE | 1969年 / 3卷 / 02期
关键词
D O I
10.1016/0006-2944(69)90004-0
中图分类号
Q5 [生物化学]; Q7 [分子生物学];
学科分类号
071010 ; 081704 ;
摘要
A wide range of ceruloplasmin concentrations was found in the sera of patients with Wilson's disease. Such sera and those of normal individuals contain small but relatively constant amounts of a colorless protein which possesses some of the properties of apoceruloplasmin. The variations in serum ceruloplasmin concentrations in patients with Wilson's disease are related primarily to the levels of the blue form of this protein. Physical, chemical and immunological measurements on ceruloplasmin isolated from the sera of these patients did not reveal differences from the protein of normal individuals. © 1969.
引用
收藏
页码:117 / &
相关论文
共 35 条
[1]   IMMUNOCHEMICAL STUDIES ON WILSONS DISEASE [J].
ARIOKA, I ;
YANAI, J ;
SANO, I ;
OGITA, Z ;
KIKKAWA, H .
CLINICA CHIMICA ACTA, 1965, 12 (03) :353-&
[2]  
BEARN AG, 1960, ANN HUM GENET, V24, P33
[3]   GENETIC AND BIOCHEMICAL ASPECTS OF WILSONS DISEASE [J].
BEARN, AG .
AMERICAN JOURNAL OF MEDICINE, 1953, 15 (04) :442-449
[4]  
CARRICO RJ, 1969, J BIOL CHEM, V244, P4141
[5]   STUDIES ON COPPER METABOLISM .29. A CRITICAL ANALYSIS OF SERUM COPPER AND CERULOPLASMIN CONCENTRATIONS IN NORMAL SUBJECTS, PATIENTS WITH WILSONS DISEASE AND RELATIVES OF PATIENTS WITH WILSONS DISEASE [J].
CARTWRIGHT, GE ;
MARKOWITZ, H ;
SHIELDS, GS ;
WINTROBE, MM .
AMERICAN JOURNAL OF MEDICINE, 1960, 28 (04) :555-563
[6]  
COHN M, 1949, J IMMUNOL, V61, P283
[7]  
DEUTSCH HF, 1964, J BIOL CHEM, V239, P3325
[8]   THE PREPARATION OF CRYSTALLINE CERULOPLASMIN FROM HUMAN PLASMA [J].
DEUTSCH, HF .
ARCHIVES OF BIOCHEMISTRY AND BIOPHYSICS, 1960, 89 (02) :225-229
[9]   RAPID METHOD FOR PREPARATION OF CRYSTALLINE HUMAN CERULOPLASMIN FROM COHN FRACTION IV-I [J].
DEUTSCH, HF ;
WALSH, DA ;
KASPER, CB .
ARCHIVES OF BIOCHEMISTRY AND BIOPHYSICS, 1962, 99 (01) :132-&
[10]   EFFECT OF ESTROGENS ON COPPER METABOLISM IN WILSONS DISEASE [J].
GERMAN, JL ;
BEARN, AG .
JOURNAL OF CLINICAL INVESTIGATION, 1961, 40 (03) :445-&