SWEAT GLAND CARCINOMA IN A PATIENT WITH SARCOIDOSIS AND PRIMARY BILIARY-CIRRHOSIS

被引:6
作者
ASVESTI, C
HADZIYANNIS, SJ
PAPADOPOULOS, S
GIAKOUMOGLOU, T
HADZIOLOU, E
TRICHIA, E
ZOGRAPHAKIS, I
机构
[1] A SYGROS HOSP,DEPT DERMATOL,ATHENS,GREECE
[2] HIPPOKRATION HOSP,ACAD DEPT MED,ATHENS,GREECE
[3] HYGIA HOSP,DEPT PATHOL,ATHENS,GREECE
[4] TZANNIO HOSP,DEPT PATHOL,PIRAEUS,GREECE
关键词
SWEAT GLAND CARCINOMA; PRIMARY BILIARY CIRRHOSIS; SARCOIDOSIS;
D O I
10.1159/000246833
中图分类号
R75 [皮肤病学与性病学];
学科分类号
100206 ;
摘要
Primary biliary cirrhosis (PBC) and sarcoidosis are both granulomatous disorders of unknown etiology. Although they are distinct clinical entities, a small number of patients presenting with manifestations of both has been reported. We describe a female patient with PBC and sarcoidosis who developed a malignant cutaneous tumor with histologic and immunohistochemical characteristics of a sweat gland carcinoma (SGC). An SGC, developing in a patient with concurrent PBC and sarcoidosis has not been reported previously.
引用
收藏
页码:198 / 202
页数:5
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