Sclerosing, pseudovascular rhabdomyosarcoma chest. Case report and literature review

Rhabdomyosarcoma is the most common sarcoma of soft tissues in childhood; in adults represents a small number of malignant tumors. It is located mainly in the head and neck, genitourinary tract, and extremities. There are several histologic types of rhabdomyosarcoma with different biological behavior. The objective is to report the case of a variety pseudovascular sclerosing rhabdomyosarcoma posterior chest wall; of which there are few cases in the world; well as a comprehensive review of the literature. A 56-year-old male attended the Unit in the presence of intrathoracic tumor documented by chest X-ray, who undergoes diagnostic protocol. Detected in thoracic tomography (CT) tumor size largely dependent left posterior thoracic wall. Subjected to tumor resection via left posterolateral thoracotomy, resecting tumor almost entirely, leaving R2. Presents with satisfactory clinical evolution and is a graduate hospital 12 days after his address. The pathology report with regards imunohistoquimica Pseudovascular sclerosing rhabdomyosarcoma with iniltration adjacent subpleural lung tissue. This is a very rare malignancy, with 15 cases reported worldwide; and which present a location never described in the literature and hence, the importance of taking into account this possibility diagnosed and knowledge for detection. 1665-9201 (C) 2014 Gaceta Mexicana de Oncologia. Publicado por Masson Doyma Mexico S.A. Todos los derechos reservados.