CONGENITAL MALTASE-SUCRASE AND MALTASE-ISOMALTASE DEFICIENCY IN AN ADULT

被引:8
|
作者
MAINGUET, P
VANDERHOEDEN, R
LOEB, H
EGGERMONT, E
机构
[1] ST PIERRE UNIV HOSP, DEPT MED, BRUSSELS, BELGIUM
[2] IXELLES HOSP, DEPT GASTROENTEROL, BRUSSELS, BELGIUM
[3] ST RAPHAEL UNIV HOSP, DEPT PEDIAT, LEUVEN, BELGIUM
[4] ST PIERRE UNIV HOSP, DEPT PEDIAT, BRUSSELS, BELGIUM
关键词
D O I
10.1159/000197335
中图分类号
R57 [消化系及腹部疾病];
学科分类号
摘要
引用
收藏
页码:353 / 359
页数:7
相关论文
共 50 条
  • [21] COMPARISON OF SPECIFICITIES OF HYDROLYSIS AND SYNTHESIS BY MALTASE AND ISOMALTASE
    LAI, H
    AXELROD, B
    FEDERATION PROCEEDINGS, 1974, 33 (05) : 1299 - 1299
  • [22] Structural analysis of human intestinal alpha-glucosydases: Sucrase-isomaltase and maltase-glucoamylase
    Nava, N.
    Rose, D.
    ACTA CRYSTALLOGRAPHICA A-FOUNDATION AND ADVANCES, 2020, 76 : A14 - A14
  • [23] Sacrosidase therapy for congenital sucrase-isomaltase deficiency
    Treem, WR
    McAdams, L
    Stanford, L
    Kastoff, G
    Justinich, C
    Hyams, J
    JOURNAL OF PEDIATRIC GASTROENTEROLOGY AND NUTRITION, 1999, 28 (02): : 137 - 142
  • [24] CONGENITAL SUCRASE AND ISOMALTASE DEFICIENCY WITH TEMPORARY LACTOSE INTOLERANCE
    MARSHALL, WC
    LLOYDSTI.J
    SEAKINS, JWT
    ACTA PAEDIATRICA SCANDINAVICA, 1967, 56 (02): : 211 - &
  • [25] A NEW CONTINUOUS OPTICAL ASSAY FOR MALTASE AND SUCRASE
    GIORGI, M
    VANNI, P
    PINZAUTI, G
    ENZYME, 1992, 46 (06) : 299 - 303
  • [26] STUDIES ON THE INTESTINAL DISACCHARIDASES OF THE PIGEON .4. IMMUNOCHEMICAL PROPERTIES OF SUCRASE.ISOMALTASE AND MALTASE.GLUCOAMYLASE
    PRAKASH, K
    PATIL, SD
    HEGDE, SN
    ARCHIVES INTERNATIONALES DE PHYSIOLOGIE DE BIOCHIMIE ET DE BIOPHYSIQUE, 1983, 91 (05): : 391 - 397
  • [27] ADULT-ONSET ACID MALTASE DEFICIENCY IN SIBLINGS
    MIYAMOTO, Y
    ETOH, Y
    JOH, R
    NODA, K
    OHYA, I
    MORIMATSU, M
    ACTA PATHOLOGICA JAPONICA, 1985, 35 (06): : 1533 - 1542
  • [28] Adult sucrase-isomaltase deficiency masquerading as IBS
    Foley, Anna
    Halmos, Emma Phoebe
    Husein, Diab M.
    Fehily, Sasha Rachel
    Loescher, Britt-Sabina
    Franke, Andre
    Naim, Hassan Y.
    Gibson, Peter R.
    D'Amato, Mauro
    GUT, 2022, 71 (06) : 1237 - +
  • [29] Molecular pathogenicity of novel sucrase-isomaltase mutations found in congenital sucrase-isomaltase deficiency patients
    Gericke, Birthe
    Amiri, Mandi
    Scott, C. Ronald
    Naim, Hassan Y.
    BIOCHIMICA ET BIOPHYSICA ACTA-MOLECULAR BASIS OF DISEASE, 2017, 1863 (03): : 817 - 826
  • [30] Identification and enzymatic characterization of the maltose-inducible α-glucosidase malL (sucrase-isomaltase-maltase) of Bacillus subtilis
    Schönert, S
    Buder, T
    Dahl, MK
    JOURNAL OF BACTERIOLOGY, 1998, 180 (09) : 2574 - 2578