X-LINKED CUTIS LAXA - DEFECTIVE CROSS-LINK FORMATION IN COLLAGEN DUE TO DECREASED LYSYL OXIDASE ACTIVITY

被引:191
作者
BYERS, PH
SIEGEL, RC
HOLBROOK, KA
NARAYANAN, AS
BORNSTEIN, P
HALL, JG
机构
[1] UNIV WASHINGTON,DEPT MED,SEATTLE,WA 98195
[2] UNIV CALIF SAN FRANCISCO,DEPT MED,SAN FRANCISCO,CA 94143
[3] UNIV WASHINGTON,DEPT BIOL STRUCT,SEATTLE,WA 98195
[4] UNIV WASHINGTON,DEPT PEDIAT,SEATTLE,WA 98195
[5] UNIV CALIF SAN FRANCISCO,DEPT ORTHOPED SURG,SAN FRANCISCO,CA 94143
[6] UNIV WASHINGTON,DEPT BIOCHEM,SEATTLE,WA 98195
[7] CHILDRENS ORTHOPED HOSP & MED CTR,SEATTLE,WA 98105
关键词
D O I
10.1056/NEJM198007103030201
中图分类号
R5 [内科学];
学科分类号
1002 ; 100201 ;
摘要
引用
收藏
页码:61 / 65
页数:5
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