Recurrent pediatric aggressive fibromatosis of the head and neck with vocal cord paralysis: A case report and review

被引:0
作者
Kulbersh, Brian D. [1 ]
Wiatrak, Brian J. [1 ]
机构
[1] Childrens Hosp Alabama, Dept Pediat Otolaryngol Head & Neck Surg, Birmingham, AL USA
关键词
Aggressive fibromatosis; Vocal cord paralysis;
D O I
10.1016/j.pedex.2010.07.005
中图分类号
R72 [儿科学];
学科分类号
100202 ;
摘要
Aggressive fibrosis (AF), a fibrous tissue proliferation disorder, is rare and benign but locally aggressive and has a high recurrence rate. A 13-year-old boy with a 9-year history of recurrent AF of the neck previously treated by surgery, chemotherapy, Celebrex, Tamoxifen, and Imatinib presented with another recurrence, this time with hoarseness and ipsilateral vocal cord paralysis. The tumor was extensively debulked but complete surgical resection was impossible and tracheostomy was required. Review of the pediatric literature found no previous case of AF with cranial nerve dysfunction. The high morbidity and recalcitrance of AF to numerous treatments warrants further research. (C) 2010 Elsevier Ireland Ltd. All rights reserved.
引用
收藏
页码:182 / 184
页数:3
相关论文
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