Right pulmonary venous atresia: a case report and review of literature

被引:5
作者
Bozbas, Serife Savas [1 ]
Varan, Birgul [2 ]
Akcay, Sule [1 ]
机构
[1] Baskent Univ, Tip Fak, Gogus Hastaliklari Anabilim Dali, Ankara, Turkey
[2] Baskent Univ, Tip Fak, Pediat Kardiyol Bilim Dali, Ankara, Turkey
来源
TUBERKULOZ VE TORAK-TUBERCULOSIS AND THORAX | 2012年 / 60卷 / 03期
关键词
Pulmonary venous atresia; recurrent pulmonary infection; pulmonary angiography;
D O I
10.5578/tt.2425
中图分类号
R56 [呼吸系及胸部疾病];
学科分类号
摘要
Isolated pulmonary vein atresia without associated congenital malformation is a very rare condition in adults. It is associated with significant mortality and morbidity. Recurrent pulmonary infections, dyspnea on exertion and hemoptysis may be the presenting complaints. Owing to the limited number of patients with this condition there may be some difficulties in it's diagnosis and therapy. We report an adult case with this rare congenital malformation and discuss it's diagnosis and management options.
引用
收藏
页码:254 / 257
页数:4
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