INTRACRANIAL XANTHOGRANULOMA OF THE DURA IN HAND-SCHULLER-CHRISTIAN DISEASE - CASE-REPORT

被引:16
作者
JAMJOOM, ZAB
RAINA, V
ALJAMALI, A
JAMJOOM, AB
YACUB, B
SHARIF, HS
机构
[1] KING SAUD UNIV,COLL MED,DIV NEUROL,RIYADH 11461,SAUDI ARABIA
[2] KING SAUD UNIV,COLL MED,DEPT PATHOL,RIYADH 11461,SAUDI ARABIA
[3] RIYADH ARMED FORCES HOSP,DEPT RADIOL & IMAGING,RIYADH,SAUDI ARABIA
关键词
HAND-SCHULLER-CHRISTIAN DISEASE; LANGERHANS CELL; WEBER-CHRISTIAN DISEASE; XANTHOGRANULOMA;
D O I
10.3171/jns.1993.78.2.0297
中图分类号
R74 [神经病学与精神病学];
学科分类号
摘要
The authors describe a 37-year-old man with the classic clinical features of Hand-Schuller-Christian disease. He presented with symptoms of increased intracranial pressure due to obstructive hydrocephalus secondary to a huge xanthogranuloma involving falx cerebri and tentorium cerebelli. Immunohistochemical and ultrastructural studies failed to demonstrate Langerhans histiocytes, however. The implication of this finding is discussed in light of the recent relevant literature.
引用
收藏
页码:297 / 300
页数:4
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