PHOSPHORYLATION OF LYSOSOMAL-ENZYMES IN FIBROBLASTS - MARKED DEFICIENCY OF N-ACETYLGLUCOSAMINE-1-PHOSPHOTRANSFERASE IN FIBROBLASTS OF PATIENTS WITH MUCOLIPIDOSIS-III

被引：20

作者：

WAHEED, A

HASILIK, A

CANTZ, M

VONFIGURA, K

机构：

来源：

HOPPE-SEYLERS ZEITSCHRIFT FUR PHYSIOLOGISCHE CHEMIE | 1982年 / 363卷 / 02期

关键词：

D O I：

10.1515/bchm2.1982.363.1.169

中图分类号：

Q5 [生物化学]; Q7 [分子生物学];

学科分类号：

071010 ; 081704 ;

摘要：

引用

页码：169 / 178

页数：10

共 12 条

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[10] FIBROBLASTS FROM PATIENTS WITH I-CELL DISEASE AND PSEUDO-HURLER POLYDYSTROPHY ARE DEFICIENT IN URIDINE 5'-DIPHOSPHATE-N-ACETYLGLUCOSAMINE - GLYCOPROTEIN N-ACETYLGLUCOSAMINYLPHOSPHOTRANSFERASE ACTIVITY [J].

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