Uterus didelphys and vaginal duplication with unilateral obstruction and ipsilateral renal agenesis

Developmental abnormalities of the uterus are common anomalies. Complete mullerian duplication with unilateral imperforate vagina is rare. Unilateral renal agenesis is a common association. This anomaly is probably secondary to a wolffian duct anomaly. A 14year-old girl presented to the emergency unite complaining vulvar odem, erratum, and dysurie. Three days ago, she had an operation because of vulvar mass in a private hospital. There was a Foley sound trough the incisional opening on the right next to the hymen and intro-ituse vagina. Pelvic examination, ultrasonography and magnetic resonance imaging (MRI) established a diagnosis of uterus didelphys with unilateral imperforate vagina and ipsilateral renal agenesis. After medical treatment of vulvar and urinary infection, an incision was performed throughout vaginal septum, which showed single vagina. A greater awareness and prompt diagnosis of this anomaly can allow for early and appropriate surgical intervention.