Biliary atresia: Where do we stand now?

被引:27
作者
Govindarajan, Krishna Kumar [1 ]
机构
[1] Jawaharlal Inst Postgrad Med Educ & Res, Dept Pediat Surg, Pondicherry Rd, Pondicherry 605006, India
关键词
Biliary atresia; Neonatal cholestasis; Kasai procedure; Neonatal jaundice; Hyperbilirubinemia;
D O I
10.4254/wjh.v8.i36.1593
中图分类号
R57 [消化系及腹部疾病];
学科分类号
摘要
The pathway from clinical suspicion to establishing the diagnosis of biliary atresia in a child with jaundice is a daunting task. However, investigations available help to point towards the correct diagnosis in reasonable time frame. Imaging by Sonography has identified several parameters which can be of utility in the diagnostic work up. Comparison of Sonography with imaging by Nuclear medicine can bring out the significant differences and also help in appropriate imaging. The battery of Biochemical tests, available currently, enable better understanding of the line-up of investigations in a given child with neonatal cholestasis. Management protocols enable standardized care with optimal outcome. The place of surgical management in biliary atresia is undisputed, although Kasai procedure and primary liver transplantation have been pitted against each other. This article functions as a platform to bring forth the various dimensions of biliary atresia.
引用
收藏
页码:1593 / 1601
页数:9
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