DIAGNOSIS OF RESPIRATORY-CHAIN DEFECTS USING H-1-NMR SPECTROSCOPY INVITRO

被引:2
|
作者
RAFTER, JEM
CHALMERS, RA
JOHNSON, A
ILES, RA
机构
[1] UNIV LONDON LONDON HOSP,COLL MED,MED UNIT,LONDON E1 1BB,ENGLAND
[2] ST GEORGE HOSP,SCH MED,DEPT CHILD HLTH,LONDON SW17 0RE,ENGLAND
[3] QUEEN ELIZABETH HOSP,DEPT CLIN BIOCHEM,LONDON E2 8PS,ENGLAND
关键词
D O I
10.1042/bst0180551
中图分类号
Q5 [生物化学]; Q7 [分子生物学];
学科分类号
071010 ; 081704 ;
摘要
引用
收藏
页码:551 / 552
页数:2
相关论文
共 50 条
  • [1] DIAGNOSIS OF MUCOPOLYSACCHARIDOSES USING H-1-NMR SPECTROSCOPY OF GLYCOSAMINOGLYCANS
    SAVAGE, AV
    APPLEGARTH, DA
    CARBOHYDRATE RESEARCH, 1986, 149 (02) : 471 - 474
  • [2] DEFECTS OF THE RESPIRATORY-CHAIN
    BINDOFF, LA
    TURNBULL, DM
    BAILLIERES CLINICAL ENDOCRINOLOGY AND METABOLISM, 1990, 4 (03): : 583 - 619
  • [3] H-1-NMR SPECTROSCOPY OF DNA
    FEIGON, J
    SKLENAR, V
    WANG, E
    GILBERT, DE
    MACAYA, RF
    SCHULTZE, P
    METHODS IN ENZYMOLOGY, 1992, 211 : 235 - 253
  • [4] BIOLOGICAL H-1-NMR SPECTROSCOPY
    PETROFF, OAC
    COMPARATIVE BIOCHEMISTRY AND PHYSIOLOGY B-BIOCHEMISTRY & MOLECULAR BIOLOGY, 1988, 90 (02): : 249 - 260
  • [5] INVITRO STUDY OF THE BINDING OF TERBIUM TO TRYPTOPHAN BY H-1-NMR AND FLUORESCENCE SPECTROSCOPY
    AIZAWA, K
    OHHATA, S
    NISHIE, H
    OHSAKA, A
    KATO, K
    MATSUSHITA, K
    HIOKA, K
    BIOCHEMICAL AND BIOPHYSICAL RESEARCH COMMUNICATIONS, 1987, 146 (02) : 791 - 796
  • [6] STRUCTURAL ASSIGNMENT OF ISOMERIC CHAIN DEMETHYLATED RETINALS BY H-1-NMR SPECTROSCOPY
    BROEK, AD
    COURTIN, JML
    MELLEMA, JR
    LUGTENBURG, J
    NICOLAY, K
    DIJKSTRA, K
    KAPTEIN, R
    ORGANIC MAGNETIC RESONANCE, 1982, 19 (02): : 105 - 107
  • [7] INBORN AND INDUCED DEFECTS OF THE MITOCHONDRIAL RESPIRATORY-CHAIN
    SCHAPIRA, AHV
    COOPER, JM
    BIOCHEMICAL SOCIETY TRANSACTIONS, 1994, 22 (04) : 996 - 1001
  • [8] Pontocerebellar hypoplasia associated with respiratory-chain defects
    de Koning, TJ
    de Vries, LS
    Groenendaal, F
    Ruitenbeek, W
    Jansen, GH
    Poll-The, BT
    Barth, PG
    NEUROPEDIATRICS, 1999, 30 (02) : 93 - 95
  • [9] H-1-NMR SPECTROSCOPY OF PYRROLIZIDINE ALKALOIDS
    SEGALL, HJ
    DALLAS, JL
    PHYTOCHEMISTRY, 1983, 22 (05) : 1271 - 1273
  • [10] THE MOLECULAR PATHOLOGY OF HUMAN RESPIRATORY-CHAIN DEFECTS
    MORGANHUGHES, JA
    COOPER, JM
    SCHAPIRA, AHV
    SWEENY, M
    HOLT, IJ
    HARDING, AE
    CLARK, JB
    REVUE NEUROLOGIQUE, 1991, 147 (6-7) : 450 - 454