HYDROMETROCOLPOS FOLLOWING PRENATAL DEXAMETHASONE TREATMENT FOR CONGENITAL ADRENAL-HYPERPLASIA (21-HYDROXYLASE DEFICIENCY)

被引:13
作者
COUPER, JJ
HUTSON, JM
WARNE, GL
机构
[1] ROYAL CHILDRENS HOSP,DEPT ENDOCRINOL & DIABET,PARKVILLE,VIC 3052,AUSTRALIA
[2] ROYAL CHILDRENS HOSP,DEPT GEN SURG,PARKVILLE,VIC 3052,AUSTRALIA
关键词
CONGENITAL ADRENAL HYPERPLASIA; 21-HYDROXYLASE DEFICIENCY; HYDROMETROCOLPOS; DEXAMETHASONE;
D O I
10.1007/BF02072507
中图分类号
R72 [儿科学];
学科分类号
100202 ;
摘要
A female with congenital adrenal hyperplasia (21-hydroxylase deficiency) received prenatal dexamethasone treatment. Suppression of the fetal adrenal was initially inadequate but adequate in later pregnancy. The baby showed masculinisation without clitoral enlargement and a narrow urogenital sinus with resulting hydrometrocolpos. It is possible that dexamethasone treatment which is initially inadequate increases the risk of this latter complication.
引用
收藏
页码:9 / 11
页数:3
相关论文
共 13 条
[1]   PRENATAL TREATMENT OF CONGENITAL ADRENAL-HYPERPLASIA RESULTING FROM 21-HYDROXYLASE DEFICIENCY [J].
DAVID, M ;
FOREST, MG .
JOURNAL OF PEDIATRICS, 1984, 105 (05) :799-803
[2]   FETAL PHALLIC GROWTH AND PENILE STANDARDS FOR NEWBORN MALE INFANTS [J].
FELDMAN, KW ;
SMITH, DW .
JOURNAL OF PEDIATRICS, 1975, 86 (03) :395-398
[3]  
FOREST MG, 1987, ANN ENDOCRINOL-PARIS, V48, P31
[4]   PRENATAL TREATMENT IN CONGENITAL ADRENAL-HYPERPLASIA DUE TO 21-HYDROXYLASE DEFICIENCY - UP-DATE 88 OF THE FRENCH MULTICENTRIC STUDY [J].
FOREST, MG ;
BETUEL, H ;
DAVID, M .
ENDOCRINE RESEARCH, 1989, 15 (1-2) :277-301
[5]   ELEVATED AMNIOTIC-FLUID CONCENTRATION OF 17 ALPHA-HYDROXYPROGESTERONE IN CONGENITAL ADRENAL-HYPERPLASIA [J].
FRASIER, SD ;
THORNEYCROFT, IH ;
WEISS, BA ;
HORTON, R .
JOURNAL OF PEDIATRICS, 1975, 86 (02) :310-312
[6]  
HAAN EA, 1992, MED J AUSTRALIA, V156, P132
[7]   URINOMA OF THE FALLOPIAN-TUBE IN VIRILIZING CONGENITAL ADRENAL-HYPERPLASIA [J].
KAUFMAN, FR ;
HARDY, BE ;
LAW, BS ;
COSTIN, G .
JOURNAL OF PEDIATRICS, 1986, 109 (03) :495-496
[8]   PRENATAL TREATMENT OF CONGENITAL ADRENAL-HYPERPLASIA - REPORT OF A NEW CASE [J].
LOEUILLE, GA ;
DAVID, M ;
FOREST, MG .
EUROPEAN JOURNAL OF PEDIATRICS, 1990, 149 (04) :237-240
[9]  
MALAIKAL RM, 1987, NEW ENGL J MED, V316, P178
[10]   POSTERIOR URETHROVAGINAL COMMUNICATION IN APPARENT MALES WITH CONGENITAL ADRENOCORTICAL HYPERPLASIA [J].
ROSENBERG, B ;
HENDREN, WH ;
CRAWFORD, JD .
NEW ENGLAND JOURNAL OF MEDICINE, 1969, 280 (03) :131-+