DEFICIENT RED-CELL SPECTRIN IN SEVERE, RECESSIVELY INHERITED SPHEROCYTOSIS

被引:176
作者
AGRE, P [1 ]
ORRINGER, EP [1 ]
BENNETT, V [1 ]
机构
[1] N CAROLINA MEM HOSP,DEPT MED,CHAPEL HILL,NC 27514
关键词
D O I
10.1056/NEJM198205133061906
中图分类号
R5 [内科学];
学科分类号
1002 ; 100201 ;
摘要
引用
收藏
页码:1155 / 1161
页数:7
相关论文
共 32 条
[1]   A MOLECULAR DEFECT IN 2 FAMILIES WITH HEMOLYTIC POIKILOCYTIC ANEMIA - REDUCTION OF HIGH-AFFINITY MEMBRANE-BINDING SITES FOR ANKYRIN [J].
AGRE, P ;
ORRINGER, EP ;
CHUI, DHK ;
BENNETT, V .
JOURNAL OF CLINICAL INVESTIGATION, 1981, 68 (06) :1566-1576
[2]  
BARTLETT GR, 1959, J BIOL CHEM, V234, P466
[3]   ERYTHROCYTE ANKYRIN - IMMUNOREACTIVE ANALOGS ARE ASSOCIATED WITH MITOTIC STRUCTURES IN CULTURED-CELLS AND WITH MICROTUBULES IN BRAIN [J].
BENNETT, V ;
DAVIS, J .
PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA-BIOLOGICAL SCIENCES, 1981, 78 (12) :7550-7554
[4]  
BENNETT V, 1979, J BIOL CHEM, V254, P2533
[5]  
BENNETT V, 1980, J BIOL CHEM, V255, P6424
[6]  
BENNETT V, 1980, J BIOL CHEM, V255, P2540
[7]  
BENNETT V, 1977, J BIOL CHEM, V252, P2753
[8]   IMMUNOREACTIVE FORMS OF HUMAN-ERYTHROCYTE ANKYRIN ARE PRESENT IN DIVERSE CELLS AND TISSUES [J].
BENNETT, V .
NATURE, 1979, 281 (5732) :597-599
[10]  
BERNSTEIN SE, 1980, LAB ANIM SCI, V30, P197