SPINAL-CORD COMPRESSION IN HOMOZYGOUS BETA-THALASSEMIA-INTERMEDIA

被引:11
作者
CARDIA, E [1 ]
TOSCANO, S [1 ]
LAROSA, G [1 ]
ZACCONE, C [1 ]
DAVELLA, D [1 ]
TOMASELLO, F [1 ]
机构
[1] UNIV MESSINA,SCH MED,PEDIAT NEUROSURG SECT,MESSINA,ITALY
关键词
EXTRAMEDULLARY HEMATOPOIESIS; BETA-THALASSEMIA; SPINAL CORD COMPRESSION; MAGNETIC RESONANCE IMAGING;
D O I
10.1159/000120785
中图分类号
R74 [神经病学与精神病学];
学科分类号
摘要
Symptomatic spinal cord compression caused by an epidural mass of extramedullary hematopoietic tissue in patients with beta-thalassemia is a rare occurrence, that becomes exceptional in childhood and adolescence. The literature is not uniform about the optimal treatment of these patients and different modes of therapy have been proposed so far, including surgical excision or decompressing laminectomy followed by local irradiation and/or hypertransfusional regimens. We report the successful treatment of such a complication in an adolescent with homozygous beta-thalassemia by surgery followed by repeated blood transfusions aimed at maintaining hematocrit at normal levels.
引用
收藏
页码:186 / 189
页数:4
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