INHIBITION BY METHYLMALONIC ACID OF MALATE TRANSPORT BY DICARBOXYLATE CARRIER IN RAT LIVER MITOCHONDRIA - POSSIBLE EXPLANATION FOR HYPOGLYCEMIA IN METHYLMALONIC ACIDURIA

被引：62
作者：
HALPERIN, ML
SCHILLER, CM
FRITZ, IB
机构：
来源：
JOURNAL OF CLINICAL INVESTIGATION | 1971年 / 50卷 / 11期
关键词：
D O I：
10.1172/JCI106725
中图分类号：
R-3 [医学研究方法]; R3 [基础医学];
学科分类号：
1001 ;
摘要：
引用
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页码：2276 / &
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共 24 条
[1]   EXPERIMENTAL VITAMIN B12 DEFICIENCY - ITS EFFECT ON TISSUE VITAMIN B12-COENZYME LEVELS AND ON METABOLISM OF METHYLMALONYL-COA [J].
CARDINALE, GJ ;
DREYFUS, PM ;
AULD, P ;
ABELES, RH .
ARCHIVES OF BIOCHEMISTRY AND BIOPHYSICS, 1969, 131 (01) :92-+
[2]  
Chappell J.B., 1967, BIOCHEMISTRY MITOCHO, P75
[3]   EFFECT OF ATRACTYLATE AND OLIGOMYCIN ON BEHAVIOUR OF MITOCHONDRIA TOWARDS ADENINE NUCLEOTIDES [J].
CHAPPELL, JB ;
CROFTS, AR .
BIOCHEMICAL JOURNAL, 1965, 95 (03) :707-&
[4]   SYSTEMS USED FOR TRANSPORT OF SUBSTRATES INTO MITOCHONDRIA [J].
CHAPPELL, JB .
BRITISH MEDICAL BULLETIN, 1968, 24 (02) :150-&
[5]  
Estabrook R.W., 1967, METHODS ENZYMOL, V10, P41, DOI [10.1016/0076-6879(67)10010-4, DOI 10.1016/0076-6879(67)10010-4]
[6]   PATHS OF CARBON IN GLUCONEOGENESIS AND LIPOGENESIS - ROLE OF MITOCHONDRIA IN SUPPLYING PRECURSORS OF PHOSPHOENOLPYRUVATE [J].
LARDY, HA ;
PAETKAU, V ;
WALTER, P .
PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA, 1965, 53 (06) :1410-&
[7]   A DERANGEMENT IN B12-METABOLISM ASSOCIATED WITH HOMOCYSTINEMIA, CYSTATHIONINEMIA, HYPOMETHIONINEMIA AND METHYLMALONIC ACIDURIA [J].
LEVY, HL ;
MUDD, SH ;
SCHULMAN, JD ;
DREYFUS, PM ;
ABELES, RH .
AMERICAN JOURNAL OF MEDICINE, 1970, 48 (03) :390-+
[8]   METHYLMALONIC ACIDEMIA - A DISORDER ASSOCIATED WITH ACIDOSIS HYPERGLYCINEMIA AND HYPERLACTATEMIA [J].
LINDBLAD, B ;
LINDBLAD, BS ;
OLIN, P ;
SVANBERG, B ;
ZETTERSTROM, R .
ACTA PAEDIATRICA SCANDINAVICA, 1968, 57 (05) :417-+
[9]  
LOWRY OH, 1951, J BIOL CHEM, V193, P265
[10]   CONGENITAL METHYLMALONIC ACIDEMIA - ENZYMATIC EVIDENCE FOR 2 FORMS OF DISEASE [J].
MORROW, G ;
BARNESS, LA ;
CARDINALE, GJ ;
ABELES, RH ;
FLAKS, JG .
PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA, 1969, 63 (01) :191-+
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