INHIBITION BY METHYLMALONIC ACID OF MALATE TRANSPORT BY DICARBOXYLATE CARRIER IN RAT LIVER MITOCHONDRIA - POSSIBLE EXPLANATION FOR HYPOGLYCEMIA IN METHYLMALONIC ACIDURIA

被引：61

作者：

HALPERIN, ML

SCHILLER, CM

FRITZ, IB

机构：

来源：

JOURNAL OF CLINICAL INVESTIGATION | 1971年 / 50卷 / 11期

关键词：

D O I：

10.1172/JCI106725

中图分类号：

R-3 [医学研究方法]; R3 [基础医学];

学科分类号：

1001 ;

摘要：

引用

收藏

页码：2276 / &

相关论文

共 24 条

[1] EXPERIMENTAL VITAMIN B12 DEFICIENCY - ITS EFFECT ON TISSUE VITAMIN B12-COENZYME LEVELS AND ON METABOLISM OF METHYLMALONYL-COA
CARDINALE, GJ
DREYFUS, PM
AULD, P
ABELES, RH
[J]. ARCHIVES OF BIOCHEMISTRY AND BIOPHYSICS, 1969, 131 (01) : 92 - +
[2] Chappell J.B., 1967, BIOCHEMISTRY MITOCHO, P75
[3] EFFECT OF ATRACTYLATE AND OLIGOMYCIN ON BEHAVIOUR OF MITOCHONDRIA TOWARDS ADENINE NUCLEOTIDES
CHAPPELL, JB
CROFTS, AR
[J]. BIOCHEMICAL JOURNAL, 1965, 95 (03) : 707 - &
[4] SYSTEMS USED FOR TRANSPORT OF SUBSTRATES INTO MITOCHONDRIA
CHAPPELL, JB
[J]. BRITISH MEDICAL BULLETIN, 1968, 24 (02) : 150 - &
[5] Estabrook R.W., 1967, METHODS ENZYMOL, V10, P41, DOI [10.1016/0076-6879(67)10010-4, DOI 10.1016/0076-6879(67)10010-4]
[6] PATHS OF CARBON IN GLUCONEOGENESIS AND LIPOGENESIS - ROLE OF MITOCHONDRIA IN SUPPLYING PRECURSORS OF PHOSPHOENOLPYRUVATE
LARDY, HA
PAETKAU, V
WALTER, P
[J]. PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA, 1965, 53 (06) : 1410 - &
[7] A DERANGEMENT IN B12-METABOLISM ASSOCIATED WITH HOMOCYSTINEMIA, CYSTATHIONINEMIA, HYPOMETHIONINEMIA AND METHYLMALONIC ACIDURIA
LEVY, HL
MUDD, SH
SCHULMAN, JD
DREYFUS, PM
ABELES, RH
[J]. AMERICAN JOURNAL OF MEDICINE, 1970, 48 (03) : 390 - +
[8] METHYLMALONIC ACIDEMIA - A DISORDER ASSOCIATED WITH ACIDOSIS HYPERGLYCINEMIA AND HYPERLACTATEMIA
LINDBLAD, B
LINDBLAD, BS
OLIN, P
SVANBERG, B
ZETTERSTROM, R
[J]. ACTA PAEDIATRICA SCANDINAVICA, 1968, 57 (05): : 417 - +
[9] LOWRY OH, 1951, J BIOL CHEM, V193, P265
[10] CONGENITAL METHYLMALONIC ACIDEMIA - ENZYMATIC EVIDENCE FOR 2 FORMS OF DISEASE
MORROW, G
BARNESS, LA
CARDINALE, GJ
ABELES, RH
FLAKS, JG
[J]. PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA, 1969, 63 (01) : 191 - +