Giant Congenital Intracranial Immature Teratoma: A Case Report and Review of Literature

Congenital intracranial tumour constitute only 0.5-1.5% and are usually associated with poor prognosis. New advancement in imaging may help in early diagnosis. We presented a case of giant fetal intracranial tumour diagnosed antenatally at 28weeks of gestation in sonography. The magnetic resonance imaging confirmed a large hetrogenous intracranial mass with bilateral ventriculomegaly. Because of the large size of the tumor and associated macrocephaly, the baby wasdelivered by caessaran section. On delivery, fetal head size was 44.5cm with wide suture and left facial nerve was involved. Ventriculoeritoneal shunt was inserted on 4th postnatal day, however complete surgical resection of tumour was not performed because of parents refusal. Neonate had rapid increase in head size and expired on postnatal day 16th. The histopathological findings of mass demonstrated a congenital immature teratoma. Neonate expired on 16th postnatal day. Antenatal diagnosis of intracranial tumour is possible with advanced imaging modalities, however an early diagnosis before second trimester is difficult. Prognosis is generally poor and depends on size of tumour, histology and timely intervention.