GLYCOGEN-STORAGE-DISEASE TYPE-IB - INFECTIOUS COMPLICATIONS AND MEASURES FOR PREVENTION

被引：0
作者：
WENDEL, U
SCHROTEN, H
BURDACH, S
WAHN, V
机构：
来源：
EUROPEAN JOURNAL OF PEDIATRICS | 1993年 / 152卷
关键词：
GLYCOGEN STORAGE DISEASE TYPE-IB; NEUTROPENIA; CROHN-LIKE DISEASE; GRANULOCYTE-MACROPHAGE COLONY STIMULATING FACTOR TREATMENT;
D O I：
暂无
中图分类号：
R72 [儿科学];
学科分类号：
100202 ;
摘要：
A patient with glycogen storage disease (GSD) type Ib, neutrophenia, chronic inflammatory bowel disease and recurrent abscesses was treated with recombinant human granulocyte-macrophage colony stimulating factor (GM-CSF). GM-CSF (and also granulocyte colony stimulating factor) therapy markedly increased the neutrophil counts and reduced the frequency of infections and inflammation. We conclude that myeloid growth factors are effective for the treatment and prevention of acute infections and chronic inflammatory complications in patients with GSD Ib.
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页码：S49 / S51
页数：3
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