LOIN PAIN-HEMATURIA SYNDROME WITH A DISTINCTIVE VASCULAR LESION AND ALTERNATIVE PATHWAY COMPLEMENT ACTIVATION

被引:0
|
作者
MILLER, F [1 ]
LANE, BP [1 ]
KIRSCH, M [1 ]
ILAMATHI, E [1 ]
MOORE, B [1 ]
FINGER, M [1 ]
机构
[1] SUNY STONY BROOK,SCH MED,DEPT MED,STONY BROOK,NY 11794
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中图分类号
R446 [实验室诊断]; R-33 [实验医学、医学实验];
学科分类号
1001 ;
摘要
We describe a 48-year-old woman with loin pain-hematuria syndrome. Her renal abnormalities included conspicuous microaneurysmal and glomeruloid (plexiform) angiomatous changes. The deposition of both properdin and the C5b-9 complex, as well as the usual C3, in arterioles argues for complement activation. To our knowledge, neither of these features has been previously described. We speculate about the cause of loin pain-hematuria syndrome and note the uncommonness of this entity in the United States as opposed to Great Britain.
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页码:1016 / 1019
页数:4
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