THE ASSOCIATION OF WILMS-TUMOR WITH NEPHROLOGIC DISEASE

被引:3
|
作者
TANK, ES [1 ]
MELVIN, T [1 ]
机构
[1] OREGON HLTH SCI UNIV,DIV UROL SURG,PORTLAND,OR 97201
关键词
Male pseudohermaphroditism; mesangial sclerosis; Wilms' tumor;
D O I
10.1016/S0022-3468(05)80005-3
中图分类号
R72 [儿科学];
学科分类号
100202 ;
摘要
Three cases of nephrologic disease characterized clinically by nephrotic syndrome and histologically with mesangial sclerosis associated with Wilms' tumor are documented. Two children were born with ambiguous genitalia and an XY chromosome constitution. A third patient had a 46,XY karyotype and developed a Wilms' tumor but had a normal female phonotype. The evaluation and current management of this syndrome are discussed. © 1990 W.B. Saunders Company.
引用
收藏
页码:724 / 725
页数:2
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