COAL-BLACK HYPERPIGMENTATION AT BIRTH IN A CHILD WITH CONGENITAL ADRENAL HYPOPLASIA

被引:9
作者
JONES, D
KAY, M
CRAIGEN, W
MCCABE, E
HAWKINS, H
DOMINEY, A
机构
[1] BAYLOR COLL MED,INST MOLEC GENET,HOUSTON,TX 77030
[2] BAYLOR COLL MED,DEPT PEDIAT,HOUSTON,TX 77030
[3] BAYLOR COLL MED,DEPT PATHOL,HOUSTON,TX 77030
[4] BAYLOR COLL MED,DEPT DERMATOL,HOUSTON,TX 77030
关键词
D O I
10.1016/0190-9622(95)91426-9
中图分类号
R75 [皮肤病学与性病学];
学科分类号
100206 ;
摘要
Congenital adrenal hypoplasia has been estimated to occur in approximately 1 of 12,500 births. Hyperpigmentation associated with this condition typically appears gradually during a period of months to years. We describe a newborn infant with profound hyperpigmentation in whom adrenal crisis subsequently developed as a result of congenital adrenal hypoplasia.
引用
收藏
页码:323 / 326
页数:4
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