BIOCHEMICAL AND IMMUNOLOGICAL STUDIES OF FIBROBLASTS DERIVED FROM A PATIENT WITH EHLERS-DANLOS SYNDROME TYPE-IV DEMONSTRATE REDUCED TYPE-III COLLAGEN-SYNTHESIS

被引：32

作者：

AUMAILLEY, M

KRIEG, T

DESSAU, W

MULLER, PK

TIMPL, R

BRICAUD, H

机构：

[1] MAX PLANCK INST BIOCHEM, D-8033 MARTINSRIED, FED REP GER

[2] UNIV MUNICH, DERMATOL KLIN, D-8000 MUNICH 22, FED REP GER

来源：

ARCHIVES OF DERMATOLOGICAL RESEARCH | 1980年 / 269卷 / 02期

关键词：

D O I：

10.1007/BF00406537

中图分类号：

R75 [皮肤病学与性病学];

学科分类号：

100206 ;

摘要：

引用

页码：169 / 177

页数：9

共 25 条

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[9] SYNTHESIS OF COLLAGEN BY HUMAN-FIBROBLASTS AND THEIR SV40 TRANSFORMANTS [J].

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[10] AMINOTERMINAL EXTENSION PEPTIDES FROM TYPE-I PROCOLLAGEN NORMALIZE EXCESSIVE COLLAGEN-SYNTHESIS OF SCLERODERMA FIBROBLASTS [J].

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