WILSONS DISEASE - INBORN ERROR OF METABOLISM WITH MULTIPLE MANIFESTATIONS

被引:133
作者
BEARN, AG
机构
关键词
D O I
10.1016/0002-9343(57)90125-0
中图分类号
R5 [内科学];
学科分类号
1002 ; 100201 ;
摘要
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页码:747 / 757
页数:11
相关论文
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[1]   ABNORMALITIES OF COPPER METABOLISM IN WILSONS DISEASE AND THEIR RELATIONSHIP TO THE AMINOACIDURIA [J].
BEARN, AG ;
KUNKEL, HG .
JOURNAL OF CLINICAL INVESTIGATION, 1954, 33 (03) :400-409
[2]   PROBLEM OF CHRONIC LIVER DISEASE IN YOUNG WOMEN [J].
BEARN, AG ;
KUNKEL, HG ;
SLATER, RJ .
AMERICAN JOURNAL OF MEDICINE, 1956, 21 (01) :3-15
[3]  
BEARN AG, 1955, J LAB CLIN MED, V45, P623
[4]   GENETIC AND BIOCHEMICAL ASPECTS OF WILSONS DISEASE [J].
BEARN, AG .
AMERICAN JOURNAL OF MEDICINE, 1953, 15 (04) :442-449
[5]  
BEARN AG, 1954, P SOC EXP BIOL MED, V85, P44
[6]   PLACE OF BAL IN THE THERAPY OF WILSONS DISEASE [J].
BEARN, AG .
AMERICAN JOURNAL OF MEDICINE, 1956, 21 (01) :134-134
[7]   VERSUCHE ZUR COERULOPLASMINSUBSTITUTION BEI DER HEPATOCEREBRALEN DEGENERATION (WILSONSCHE KRANKHEIT) [J].
BICKEL, H ;
SCHULTZE, HE ;
GRUTER, W ;
GOLLNER, I .
KLINISCHE WOCHENSCHRIFT, 1956, 34 (35-6) :961-968
[8]  
BISHOP C, 1954, P SOC EXP BIOL MED, V86, P440
[9]   STUDIES ON COPPER METABOLISM .16. RADIOACTIVE COPPER STUDIES IN NORMAL SUBJECTS AND IN PATIENTS WITH HEPATOLENTICULAR DEGENERATION [J].
BUSH, JA ;
MAHONEY, JP ;
MARKOWITZ, H ;
GUBLER, CJ ;
CARTWRIGHT, GE ;
WINTROBE, MM .
JOURNAL OF CLINICAL INVESTIGATION, 1955, 34 (12) :1766-1778
[10]   STUDIES ON COPPER METABOLISM .13. HEPATOLENTICULAR DEGENERATION [J].
CARTWRIGHT, GE ;
HODGES, RE ;
GUBLER, CJ ;
MAHONEY, JP ;
DAUM, K ;
WINTROBE, MM ;
BEAN, WB .
JOURNAL OF CLINICAL INVESTIGATION, 1954, 33 (11) :1487-1501