ENZYMES OF UREA SYNTHESIS IN FAMILIAL PROTEIN INTOLERANCE WITH DEFICIENT TRANSPORT OF BASIC AMINO ACIDS

被引:28
作者
KEKOMAKI, M
RAIHA, NCR
PERHEENTUPA, J
机构
来源
ACTA PAEDIATRICA SCANDINAVICA | 1967年 / 56卷 / 06期
关键词
D O I
10.1111/j.1651-2227.1967.tb15989.x
中图分类号
R72 [儿科学];
学科分类号
100202 ;
摘要
引用
收藏
页码:631 / +
页数:1
相关论文
共 27 条
[1]  
ALLAN JD, 1958, LANCET, V1, P182
[2]  
BROWN GW, 1959, J BIOL CHEM, V234, P1769
[3]   IMPROVED METHOD FOR THE MICRODETERMINATION OF ARGININE BY USE OF 8-HYDROXYQUINOLINE [J].
CERIOTTI, G ;
SPANDRIO, L .
BIOCHEMICAL JOURNAL, 1957, 66 (04) :603-607
[4]  
COLOMBO JP, 1964, LANCET, V1, P1014
[6]   THE PREVENTION OF AMMONIA TOXICITY BY L-ARGININE AND RELATED COMPOUNDS [J].
GREENSTEIN, JP ;
WINITZ, M ;
GULLINO, P ;
BIRNBAUM, SM .
ARCHIVES OF BIOCHEMISTRY AND BIOPHYSICS, 1955, 59 (01) :302-303
[7]   THE TOXICITY OF ESSENTIAL AMINO ACID MIXTURES WITH SPECIAL REFERENCE TO THE PROTECTIVE EFFECT OF L-ARGININE [J].
GULLINO, P ;
WINITZ, M ;
BIRNBAUM, SM ;
OTEY, MC ;
CORNFIELD, J ;
GREENSTEIN, JP .
ARCHIVES OF BIOCHEMISTRY AND BIOPHYSICS, 1955, 58 (01) :255-257
[8]  
HUNTER A, 1945, J BIOL CHEM, V157, P427
[9]   FAMILIAL PROTEIN INTOLERANCE WITH DEFICIENT TRANSPORT OF BASIC AMINO ACIDS - AN ANALYSIS OF 10 PATIENTS [J].
KEKOMAKI, M ;
VISAKORPI, JK ;
PERHEENTUPA, J ;
SAXEN, L .
ACTA PAEDIATRICA SCANDINAVICA, 1967, 56 (06) :617-+
[10]  
KEKOMAKI M, 1967, SCAND J CLIN LAB INV, VS 19, P89