ADENOSINE-DEAMINASE DEFICIENCY - DISAPPEARANCE OF ADENINE DEOXYNUCLEOTIDES FROM A PATIENTS ERYTHROCYTES AFTER SUCCESSFUL MARROW TRANSPLANTATION

被引：50

作者：

CHEN, SH

OCHS, HD

SCOTT, CR

GIBLETT, ER

TINGLE, AJ

机构：

[1] UNIV BRITISH COLUMBIA,FAC MED,DEPT PEDIAT,VANCOUVER V6T 1W5,BC,CANADA

[2] PUGET SOUND BLOOD CTR,SEATTLE,WA 98104

来源：

JOURNAL OF CLINICAL INVESTIGATION | 1978年 / 62卷 / 06期

关键词：

D O I：

10.1172/JCI109259

中图分类号：

R-3 [医学研究方法]; R3 [基础医学];

学科分类号：

1001 ;

摘要：

引用

页码：1386 / 1389

页数：4

共 15 条

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[2]

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[3]

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[4]

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[5] DEOXYADENOSINE TRIPHOSPHATE AS A POTENTIALLY TOXIC METABOLITE IN ADENOSINE-DEAMINASE DEFICIENCY [J].

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[6]

COLEMAN MS, 1978, J BIOL CHEM, V253, P1619

[7] OVERPRODUCTION OF ADENINE DEOXYNUCLEOSIDES AND DEOXYNUCLEOTIDES IN ADENOSINE-DEAMINASE DEFICIENCY WITH SEVERE COMBINED IMMUNODEFICIENCY DISEASE [J].

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JOURNAL OF CLINICAL INVESTIGATION, 1978, 62 (04) :884-887

[8]

GIBLETT ER, 1972, LANCET, V2, P1067

[9]

Meuwissen HJ, 1975, COMBINED IMMUNODEFIC

[10] PURINE METABOLISM IN ADENOSINE-DEAMINASE DEFICIENCY [J].

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GOLDBLUM, RM .

PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA, 1976, 73 (08) :2867-2871

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