GLUTATHIONE METABOLISM IN THE LUNG - INHIBITION OF ITS SYNTHESIS LEADS TO LAMELLAR BODY AND MITOCHONDRIAL DEFECTS

被引:155
作者
MARTENSSON, J [1 ]
JAIN, A [1 ]
FRAYER, W [1 ]
MEISTER, A [1 ]
机构
[1] CORNELL UNIV,MED CTR,COLL MED,DEPT PEDIAT,NEW YORK,NY 10021
关键词
D O I
10.1073/pnas.86.14.5296
中图分类号
O [数理科学和化学]; P [天文学、地球科学]; Q [生物科学]; N [自然科学总论];
学科分类号
07 ; 0710 ; 09 ;
摘要
引用
收藏
页码:5296 / 5300
页数:5
相关论文
共 34 条
[1]  
Altman P.L., 1974, BIOL DATA BOOK, P1598
[2]  
ANDERSON ME, 1980, J BIOL CHEM, V255, P9530
[3]   GLUTATHIONE MONOETHYL ESTER - PREPARATION, UPTAKE BY TISSUES, AND CONVERSION TO GLUTATHIONE [J].
ANDERSON, ME ;
POWRIE, F ;
PURI, RN ;
MEISTER, A .
ARCHIVES OF BIOCHEMISTRY AND BIOPHYSICS, 1985, 239 (02) :538-548
[4]   DIRECT EVIDENCE FOR INTER-ORGAN TRANSPORT OF GLUTATHIONE AND THAT THE NON-FILTRATION RENAL MECHANISM FOR GLUTATHIONE UTILIZATION INVOLVES GAMMA-GLUTAMYL-TRANSFERASE TRANSPEPTIDASE [J].
ANDERSON, ME ;
BRIDGES, RJ ;
MEISTER, A .
BIOCHEMICAL AND BIOPHYSICAL RESEARCH COMMUNICATIONS, 1980, 96 (02) :848-853
[5]  
ANDERSON ME, 1985, METHOD ENZYMOL, V113, P550
[6]  
[Anonymous], 1983, FUNCTIONS GLUTATHION
[7]   GLUTATHIONE BIOSYNTHESIS IN THE ISOLATED PERFUSED RAT LUNG - UTILIZATION OF EXTRACELLULAR GLUTATHIONE [J].
BERGGREN, M ;
DAWSON, J ;
MOLDEUS, P .
FEBS LETTERS, 1984, 176 (01) :189-192
[8]  
Boyum A., 1968, SCAND J CLIN LAB INV, V97, P7
[9]  
BRADFORD MM, 1976, ANAL BIOCHEM, V72, P248, DOI 10.1016/0003-2697(76)90527-3
[10]   NORMAL ALVEOLAR EPITHELIAL LINING FLUID CONTAINS HIGH-LEVELS OF GLUTATHIONE [J].
CANTIN, AM ;
NORTH, SL ;
HUBBARD, RC ;
CRYSTAL, RG .
JOURNAL OF APPLIED PHYSIOLOGY, 1987, 63 (01) :152-157