EFFECT OF THIAMINE TREATMENT ON ACTIVITY OF PYRUVATE DEHYDROGENASE - RELATION TO TREATMENT OF LEIGHS ENCEPHALOMYELOPATHY

被引：18

作者：

HOMMES, FA ^{[1
]}

BERGER, R ^{[1
]}

LUITDEHA.G ^{[1
]}

机构：

[1] UNIV GRONINGEN, SCH MED, DEPT PEDIATR, LAB DEV BIOCHEM, GRONINGEN, NETHERLANDS

来源：

PEDIATRIC RESEARCH | 1973年 / 7卷 / 07期

关键词：

D O I：

10.1203/00006450-197307000-00003

中图分类号：

R72 [儿科学];

学科分类号：

100202 ;

摘要：

引用

页码：616 / 619

页数：4

共 18 条

[1]

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[3] THIAMINE TRIPHOSPHATE DEFICIENCY IN SUBACUTE NECROTIZING ENCEPHALOMYELOPATHY [J].

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ITOKAWA, Y ;

PINCUS, JH .

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[4] EXPERIENCE WITH PHOSPHORYL TRANSFERASE INHIBITION IN SUBACUTE NECROTIZING ENCEPHALOMYELOPATHY [J].

COOPER, JR ;

PINCUS, JH ;

ITOKAWA, Y ;

PIROS, K .

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[5]

DEGROOT CJ, 1972, FURTHER STUDIES LEIG, P40

[6]

DELVIN E, 1972, PEDIATR RES, V6, P392

[7] DIFFERENCES BETWEEN ATP/ADP RATIOS IN MITOCHONDRIAL MATRIX AND IN EXTRAMITOCHONDRIAL SPACE [J].

HELDT, HW ;

MILOVANCEV, M ;

KLINGENBERG, M .

EUROPEAN JOURNAL OF BIOCHEMISTRY, 1972, 30 (03) :434-+

[8] LEIGHS ENCEPHALOMYELOPATHY - AN INBORN ERROR OF GLUCONEOGENESIS [J].

HOMMES, FA ;

POLMAN, HA ;

REERINK, JD .

ARCHIVES OF DISEASE IN CHILDHOOD, 1968, 43 (230) :423-&

[9]

HOMMES FA, BIOCHEMISTRY INBORN

[10]

LANSDALE D, 1968, NEW ENGL J MED, V278, P1235

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