ISOVALERYL-COA DEHYDROGENASE FROM RAT-LIVER

被引：0
|
作者：
IKEDA, Y [1 ]
TANAKA, K [1 ]
机构：
[1] YALE UNIV, SCH MED, DEPT HUMAN GENET, NEW HAVEN, CT 06510 USA
来源：
METHODS IN ENZYMOLOGY | 1988年 / 166卷
关键词：
D O I：
暂无
中图分类号：
Q5 [生物化学];
学科分类号：
071010 ; 081704 ;
摘要：
引用
收藏
页码：374 / 389
页数：16
相关论文
共 50 条
  • [21] Cloning of a gene for an acyl-CoA dehydrogenase from Pisum sativum L. and purification and characterization of its product as an isovaleryl-CoA dehydrogenase
    Reinard, T
    Janke, V
    Willard, J
    Buck, F
    Jacobsen, HJ
    Vockley, J
    JOURNAL OF BIOLOGICAL CHEMISTRY, 2000, 275 (43) : 33738 - 33743
  • [22] MUTANT ISOVALERYL-COA DEHYDROGENASE IN ISOVALERIC ACIDEMIA CELLS - ASSAY OF ACTIVITY AND MOLECULAR CHARACTERIZATION
    IKEDA, Y
    TANAKA, K
    METHODS IN ENZYMOLOGY, 1988, 166 : 155 - 166
  • [23] Structure of human isovaleryl-CoA dehydrogenase at 2.6 angstrom resolution: Basis for substrate specificity
    Tiffany, KA
    Roberts, DL
    Wang, M
    Paschke, R
    Mohsen, AWA
    Vockley, J
    Kim, JJP
    BIOCHEMISTRY, 1997, 36 (28) : 8455 - 8464
  • [24] Mitochondrial import and processing of wild type and type III mutant isovaleryl-CoA dehydrogenase
    Volchenboum, SL
    Vockley, J
    JOURNAL OF BIOLOGICAL CHEMISTRY, 2000, 275 (11) : 7958 - 7963
  • [25] THE SPECIFIC-INHIBITION OF THE PYRUVATE-DEHYDROGENASE COMPLEX FROM PIG-KIDNEY BY PROPIONYL-COA AND ISOVALERYL-COA
    GREGERSEN, N
    BIOCHEMICAL MEDICINE, 1981, 26 (01): : 20 - 27
  • [26] Three linked variants have opposing regulatory effects on isovaleryl-CoA dehydrogenase gene expression
    Brown, Elizabeth A.
    Kales, Susan
    Boyle, Michael James
    Vitti, Joseph
    Kotliar, Dylan
    Schaffner, Steve
    Tewhey, Ryan
    Sabeti, Pardis C.
    HUMAN MOLECULAR GENETICS, 2024, 33 (03) : 270 - 283
  • [27] PURIFICATION AND CHARACTERIZATION OF SHORT-CHAIN (SCAD) AND MEDIUM CHAIN ACYL-COA DEHYDROGENASES (MCAD) AND OF ISOVALERYL-COA DEHYDROGENASE (IVD) FROM HUMAN-LIVER
    FINOCCHIARO, G
    TANAKA, K
    FEDERATION PROCEEDINGS, 1986, 45 (06) : 1889 - 1889
  • [28] Enzymatic analysis of MCAD, VLCAD, glutaryl-CoA dehydrogenase (GCDH), and isovaleryl-CoA dehydrogenase (IVD) in lymphocytes with implications for neonatal screening
    Wanders, R. J. A.
    Ruiter, J. P. N.
    Duran, M.
    Wijburg, F. A.
    Kulik, W.
    Waterham, H. R.
    JOURNAL OF INHERITED METABOLIC DISEASE, 2007, 30 : 5 - 5
  • [29] A Case Report of a Novel Isovaleryl-CoA Dehydrogenase Gene Mutation in a Chinese Family with Isovaleric Acidemia
    Chen, Wen
    Miao, Chenglin
    Li, Yingying
    Wang, Xia
    Wu, Wenjing
    Long, Qichen
    Jiang, Yongmei
    Yan, Ziyi
    Cui, Yali
    CLINICAL LABORATORY, 2023, 69 (09) : 1985 - 1989
  • [30] Arginine 387 of human isovaleryl-CoA dehydrogenase plays a crucial role in substrate/product binding
    Volchenboum, SL
    Mohsen, AWA
    Kim, JJP
    Vockley, J
    MOLECULAR GENETICS AND METABOLISM, 2001, 74 (1-2) : 226 - 237
12345