LANGERHANS CELL HISTIOCYTOSIS AND THE NERVOUS-SYSTEM

被引:21
作者
BURN, DJ
WATSON, JDG
RODDIE, M
CHU, AC
LEGG, NJ
FRACKOWIAK, RSJ
机构
[1] UCL NATL HOSP NEUROL & NEUROSURG, LONDON, ENGLAND
[2] HAMMERSMITH HOSP, DEPT MED, NEUROL UNIT, LONDON W12 0HS, ENGLAND
[3] HAMMERSMITH HOSP, DEPT DIAGNOST RADIOL, LONDON W12 0HS, ENGLAND
[4] HAMMERSMITH HOSP, DEPT MED, DERMATOL UNIT, LONDON W12 0HS, ENGLAND
关键词
LANGERHANS CELL HISTIOCYTOSIS; CENTRAL NERVOUS SYSTEM;
D O I
10.1007/BF00867593
中图分类号
R74 [神经病学与精神病学];
学科分类号
摘要
We report two cases of Langerhans' cell histiocytosis with unusual central nervous system (CNS) involvement. The first patient had behavioural disturbances, memory loss and diabetes insipidus. His response to a range of treatments was poor. The second patient presented with seizures and headaches suggestive of raised intracranial pressure. Etoposide (VP16) chemotherapy led to a dramatic clinical and radiologicaL improvement. The various CNS manifestations of Langerhans' cell histiocytosis and their management are discussed.
引用
收藏
页码:345 / 350
页数:6
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