INFUSION OF PURIFIED GLUCOCEREBROSIDASE INTO PATIENTS WITH GAUCHERS-DISEASE

被引:0
|
作者
PENTCHEV, PG [1 ]
BRADY, RO [1 ]
GAL, AE [1 ]
HIBBERT, SR [1 ]
DEKABAN, AS [1 ]
机构
[1] NIH,BETHESDA,MD 20014
关键词
D O I
暂无
中图分类号
Q [生物科学];
学科分类号
07 ; 0710 ; 09 ;
摘要
引用
收藏
页码:1300 / 1300
页数:1
相关论文
共 50 条
  • [1] BRAIN GLUCOCEREBROSIDASE IN GAUCHERS-DISEASE
    DANIELS, LB
    COYLE, PJ
    GLEW, RH
    RADIN, NS
    LABOW, RS
    ARCHIVES OF NEUROLOGY, 1982, 39 (09) : 550 - 556
  • [2] BRAIN GLUCOCEREBROSIDASE IN GAUCHERS-DISEASE
    DANIELS, LB
    COYLE, PJ
    GLEW, RH
    RADIN, NS
    LABOW, RS
    FEDERATION PROCEEDINGS, 1981, 40 (06) : 1761 - 1761
  • [3] MAMMALIAN GLUCOCEREBROSIDASE - IMPLICATIONS FOR GAUCHERS-DISEASE
    GLEW, RH
    BASU, A
    LAMARCO, KL
    PRENCE, EM
    LABORATORY INVESTIGATION, 1988, 58 (01) : 5 - 25
  • [4] REPLACEMENT THERAPY FOR INHERITED ENZYME DEFICIENCY - USE OF PURIFIED GLUCOCEREBROSIDASE IN GAUCHERS-DISEASE
    BRADY, RO
    PENTCHEV, PG
    GAL, AE
    HIBBERT, SR
    DEKABAN, AS
    NEW ENGLAND JOURNAL OF MEDICINE, 1974, 291 (19): : 989 - 993
  • [5] REPLACEMENT THERAPY FOR INHERITED ENZYME DEFICIENCY - SUSTAINED CLEARANCE OF ACCUMULATED GLUCOCEREBROSIDE IN GAUCHERS-DISEASE FOLLOWING INFUSION OF PURIFIED GLUCOCEREBROSIDASE
    PENTCHEV, PG
    BRADY, RO
    GAL, AE
    HIBBERT, SR
    JOURNAL OF MOLECULAR MEDICINE, 1975, 1 (01) : 73 - 78
  • [6] GAUCHERS-DISEASE IN THE PRESENCE OF NORMAL GLUCOCEREBROSIDASE ACTIVITY
    SCHOFIELD, DE
    SCOTT, CR
    LAGE, JM
    FARRELL, DF
    HUMAN PATHOLOGY, 1992, 23 (05) : 588 - 592
  • [7] CHARACTERIZATION OF LYSOSOMAL GLUCOCEREBROSIDASE IN NORMAL AND GAUCHERS-DISEASE TISSUES
    GINNS, EI
    LASZLOW, DJ
    MOORE, C
    BRADY, RO
    BARRANGER, JA
    FEDERATION PROCEEDINGS, 1983, 42 (07) : 1912 - 1912
  • [8] A MUTATION IN THE HUMAN GLUCOCEREBROSIDASE GENE IN NEURONOPATHIC GAUCHERS-DISEASE
    TSUJI, S
    CHOUDARY, PV
    MARTIN, BM
    STUBBLEFIELD, BK
    MAYOR, JA
    BARRANGER, JA
    GINNS, EI
    NEW ENGLAND JOURNAL OF MEDICINE, 1987, 316 (10): : 570 - 575
  • [9] GAUCHERS-DISEASE - THERAPY BY INTRAVENOUS INFUSIONS OF MODIFIED GLUCOCEREBROSIDASE
    BECK, M
    VALADARES, ER
    LOTZ, J
    CLINICAL INVESTIGATOR, 1993, 71 (01): : 78 - 78
  • [10] DEFICIENT GLUCOCEREBROSIDASE ACTIVITY IN GAUCHERS-DISEASE, TYPE-3
    MURPHY, JV
    GLEW, RF
    PETERS, SP
    PEDIATRIC RESEARCH, 1976, 10 (04) : 368 - 368