THE PRECURSOR OF SULFATIDE ACTIVATOR PROTEIN IS PROCESSED TO 3 DIFFERENT PROTEINS

被引:103
作者
FURST, W
MACHLEIDT, W
SANDHOFF, K
机构
[1] UNIV BONN,INST ORGAN CHEM & BIOCHEM,GERHARD DOMAGK STR 1,D-5300 BONN 1,FED REP GER
[2] UNIV MUNICH,INST PHYSIOL CHEM PHYS BIOCHEM & ZELLBIOL,D-8000 MUNICH 2,FED REP GER
来源
BIOLOGICAL CHEMISTRY HOPPE-SEYLER | 1988年 / 369卷 / 05期
关键词
D O I
10.1515/bchm3.1988.369.1.317
中图分类号
Q5 [生物化学]; Q7 [分子生物学];
学科分类号
071010 ; 081704 ;
摘要
引用
收藏
页码:317 / 328
页数:12
相关论文
共 47 条
[1]   ACTIVATOR PROTEINS FOR SULFATIDE HYDROLYSIS AND GM1-GANGLIOSIDE HYDROLYSIS - PROBABLE IDENTITY ON THE BASIS OF THEIR COPURIFICATION, PROPERTIES, LIGAND-BINDING AND IMMUNOCHEMICAL INTERACTIONS [J].
BANKS, MN ;
HERBERT, SJ ;
WYNN, CH .
GLYCOCONJUGATE JOURNAL, 1987, 4 (02) :157-170
[2]   Genetic control of biochemical reactions in neurospora [J].
Beadle, GW ;
Tatum, EL .
PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA, 1941, 27 :499-506
[3]   MECHANISM OF ACTIVATION OF GLUCOCEREBROSIDASE BY CO-BETA-GLUCOSIDASE (GLUCOSIDASE ACTIVATOR PROTEIN) [J].
BERENT, SL ;
RADIN, NS .
BIOCHIMICA ET BIOPHYSICA ACTA, 1981, 664 (03) :572-582
[4]  
Chou P Y, 1978, Adv Enzymol Relat Areas Mol Biol, V47, P45
[5]   ISOLATION OF 2 FORMS OF AN ACTIVATOR PROTEIN FOR THE ENZYMIC SPHINGOMYELIN DEGRADATION FROM HUMAN GAUCHER SPLEEN [J].
CHRISTOMANOU, H ;
KLEINSCHMIDT, T .
BIOLOGICAL CHEMISTRY HOPPE-SEYLER, 1985, 366 (03) :245-256
[6]   IMMUNOCHEMICAL CHARACTERIZATION OF 2 ACTIVATOR PROTEINS STIMULATING ENZYMATIC SPHINGOMYELIN DEGRADATION INVITRO ABSENCE OF ONE OF THEM IN A HUMAN GAUCHER DISEASE VARIANT [J].
CHRISTOMANOU, H ;
AIGNESBERGER, A ;
LINKE, RP .
BIOLOGICAL CHEMISTRY HOPPE-SEYLER, 1986, 367 (09) :879-890
[8]  
CONZELMANN E, 1987, METHOD ENZYMOL, V138, P792
[9]   PURIFICATION AND CHARACTERIZATION OF AN ACTIVATOR PROTEIN FOR THE DEGRADATION OF GLYCOLIPID-GM2 AND GLYCOLIPID-GA2 BY HEXOSAMINIDASE-A [J].
CONZELMANN, E ;
SANDHOFF, K .
HOPPE-SEYLERS ZEITSCHRIFT FUR PHYSIOLOGISCHE CHEMIE, 1979, 360 (12) :1837-1849
[10]   COMPLEXING OF GLYCOLIPIDS AND THEIR TRANSFER BETWEEN MEMBRANES BY THE ACTIVATOR PROTEIN FOR DEGRADATION OF LYSOSOMAL GANGLIOSIDE GM2 [J].
CONZELMANN, E ;
BURG, J ;
STEPHAN, G ;
SANDHOFF, K .
EUROPEAN JOURNAL OF BIOCHEMISTRY, 1982, 123 (02) :455-464