GROWTH IN ADULTHOOD AFTER LIVER-TRANSPLANTATION FOR GLYCOGEN-STORAGE-DISEASE TYPE-I

被引：31

作者：

KIRSCHNER, BS

BAKER, AL

THORP, FK

机构：

[1] WYLER CHILDRENS HOSP,DEPT PEDIAT,HEPATOL SECT,CHICAGO,IL 60637

[2] WYLER CHILDRENS HOSP,DEPT PEDIAT,NUTR & METAB SECT,CHICAGO,IL 60637

[3] UNIV CHICAGO HOSP & CLIN,DEPT MED,LIVER STUDY UNIT,CHICAGO,IL 60637

来源：

GASTROENTEROLOGY | 1991年 / 101卷 / 01期

关键词：

PLASMA SOMATOMEDIN; SEXUAL-MATURATION; CHILDREN; MANAGEMENT; THERAPY;

D O I：

10.1016/0016-5085(91)90483-2

中图分类号：

R57 [消化系及腹部疾病];

学科分类号：

摘要：

Continuation of linear growth late into the third decade of life is rarely observed. This report describes a 27-year-old man with delayed growth and sexual maturation secondary to glycogen storage disease type I who grew 5.3 cm after orthotopic liver transplantation. Sequential improvement in selected measures of metabolic control (blood glucose, lactate, and bicarbonate concentrations) and growth-promoting peptides (testosterone and insulinlike growth factor I) were documented after transplantation and before the increase in height. Potential increases in final stature may be present in adult patients with underlying metabolic disease and delayed skeletal maturation. © 1991.

引用

页码：238 / 241

页数：4