NEUROFIBROMA OF THE SUPRAGLOTTIC LARYNX IN CHILDHOOD

被引:9
作者
CZIGNER, J
FEKETESZABO, G
机构
关键词
NEUROFIBROMATOSIS; LARYNGEAL NEOPLASMS; SURGERY;
D O I
10.1017/S0022215100126155
中图分类号
R76 [耳鼻咽喉科学];
学科分类号
100213 ;
摘要
The case of a male child with a benign neurogenic laryngeal tumour caused by von Recklinghausen's disease is presented. At the age of eight years, tracheostomy was necessary. The tumour, deforming the right half of the larynx and extending into the right half of the neck, was removed three years later. Following this procedure, decannulation was possible, and the patient has been free of laryngological complaints for six years. Attention is drawn to the fact that autosomal dominantly inherited neurofibromatosis is a generalized benign tumour with a special form. If it involves any vital structure or forms a functional obstacle, meticulous surgical removal is necessary, and this provides good prospects over a long period.
引用
收藏
页码:156 / 158
页数:3
相关论文
共 11 条
[1]   GENE FOR VON RECKLINGHAUSEN NEUROFIBROMATOSIS IS IN THE PERICENTROMERIC REGION OF CHROMOSOME-17 [J].
BARKER, D ;
WRIGHT, E ;
NGUYEN, K ;
CANNON, L ;
FAIN, P ;
GOLDGAR, D ;
BISHOP, DT ;
CAREY, J ;
BATY, B ;
KIVLIN, J ;
WILLARD, H ;
WAYE, JS ;
GREIG, G ;
LEINWAND, L ;
NAKAMURA, Y ;
OCONNELL, P ;
LEPPERT, M ;
LALOUEL, JM ;
WHITE, R ;
SKOLNICK, M .
SCIENCE, 1987, 236 (4805) :1100-1102
[2]   LARYNGEAL INVOLVEMENT IN VONRECKLINGHAUSENS DISEASE - CASE-REPORT AND REVIEW OF LITERATURE [J].
CHANGLO, M .
LARYNGOSCOPE, 1977, 87 (03) :435-442
[3]  
DALY JF, 1963, ARCHIV OTOLARYNGOL, V77, P262
[4]  
HOLT RG, 1978, LARYNGOSCOPE, V88, P1627
[5]  
KARJA J, 1982, ACTA OTOLARYNGOLOG S, V386, P181
[6]  
KIMMELMAN CP, 1979, ARCH OTOLARYNGOL, V105, P732
[7]  
MCKENNAN KX, 1991, LARYNGOSCOPE, V101, P109
[8]   NEUROFIBROMA OF RECURRENT LARYNGEAL NERVE [J].
REES, G .
CHEST, 1971, 60 (04) :414-+
[9]   NEUROFIBROMA OF THE CERVICAL SYMPATHETIC CHAIN PRESENTING WITH HORNERS SYNDROME [J].
RUCKLEY, RW ;
BLAIR, RL .
JOURNAL OF LARYNGOLOGY AND OTOLOGY, 1986, 100 (12) :1433-1436
[10]   GENETIC-LINKAGE OF VONRECKLINGHAUSEN NEUROFIBROMATOSIS TO THE NERVE GROWTH-FACTOR RECEPTOR GENE [J].
SEIZINGER, BR ;
ROULEAU, GA ;
OZELIUS, LJ ;
LANE, AH ;
FARYNIARZ, AG ;
CHAO, MV ;
HUSON, S ;
KORF, BR ;
PARRY, DM ;
PERICAKVANCE, MA ;
COLLINS, FS ;
HOBBS, WJ ;
FALCONE, BG ;
IANNAZZI, JA ;
ROY, JC ;
STGEORGEHYSLOP, PH ;
TANZI, RE ;
BOTHWELL, MA ;
UPADHYAYA, M ;
HARPER, P ;
GOLDSTEIN, AE ;
HOOVER, DL ;
BADER, JL ;
SPENCE, MA ;
MULVIHILL, JJ ;
AYLSWORTH, AS ;
VANCE, JM ;
ROSSENWASSER, GOD ;
GASKELL, PC ;
ROSES, AD ;
MARTUZA, RL ;
BREAKEFIELD, XO ;
GUSELLA, JF .
CELL, 1987, 49 (05) :589-594