VARIATION OF BETA-N-ACETYLHEXOSAMINIDASE-PATTERN IN TAY-SACHS DISEASE

被引:250
作者
SANDHOFF, K
机构
[1] Max-Planck-Institut für Psychiatrie, Neurochemische Abteilung. München
关键词
D O I
10.1016/0014-5793(69)80274-7
中图分类号
Q5 [生物化学]; Q7 [分子生物学];
学科分类号
071010 ; 081704 ;
摘要
[No abstract available]
引用
收藏
页码:351 / &
相关论文
共 14 条
[1]  
BRADY RO, 1967, CLIN CHEM, V14, P565
[2]   INHIBITION OF GLYCOSIDASES BY ALDONOLACTONES OF CORRESPONDING CONFIGURATION .2. INHIBITORS OF BETA-N-ACETYLGLUCOSAMINIDASE [J].
FINDLAY, J ;
LEVVY, GA ;
MARSH, CA .
BIOCHEMICAL JOURNAL, 1958, 69 :467-476
[3]   ENZYMATIC HYDROLYSIS OF SPHINGOLIPIDS .6. HYDROLYSIS OF CERAMIDE GLYCOSIDES BY CALF BRAIN BETA-N-ACETYLHEXOSAMINIDASE [J].
FROHWEIN, YZ ;
GATT, S .
BIOCHEMISTRY, 1967, 6 (09) :2783-&
[4]   ISOLATION OF BETA-N-ACETYLHEXOSAMINIDASE BETA-N-ACETYLGLUCOSAMINIDASE AND BETA-N-ACETYLGALACTOSAMINIDASE FROM CALF BRAIN [J].
FROHWEIN, YZ ;
GATT, S .
BIOCHEMISTRY, 1967, 6 (09) :2775-&
[5]  
HARZER K, 1968, Z ANAL CHEM FRESENIU, V243, P527
[6]  
JATZKEWITZ H, 1966, SPHINGOLIPOIDOSEN, P112
[7]  
LEDEEN ROBERT, 1965, BIOCHEMISTRY, V4, P2225, DOI 10.1021/bi00886a040
[8]   N-ACETYL-BETA-GLUCOSAMINIDASES IN HUMAN SPLEEN [J].
ROBINSON, D ;
STIRLING, JL .
BIOCHEMICAL JOURNAL, 1968, 107 (03) :321-&
[9]   INFANTILE AMAUROTIC IDIOCY AND RELATED FORMS OF GANGLIOSIDE STORAGE DISEASES [J].
SANDHOFF, K ;
JATZKEWITZ, H ;
PETERS, G .
NATURWISSENSCHAFTEN, 1969, 56 (07) :356-+
[10]   RESOLVATION OF MAMMALIAN N-ACETYL-BETA-D-HEXOSAMINIDASE INTO MULTIPLE FORMS BY MEANS OF ELECTROFOCUSSING [J].
SANDHOFF, K .
HOPPE-SEYLERS ZEITSCHRIFT FUR PHYSIOLOGISCHE CHEMIE, 1968, 349 (09) :1095-&