ARRHYTHMOGENIC RIGHT VENTRICULAR DYSPLASIA

被引:1
作者
FATKIN, D
HICKIE, J
THORBURN, C
KUCHAR, D
机构
[1] ST VINCENTS HOSP,DEPT CARDIOL,SYDNEY,NSW 2010,AUSTRALIA
[2] ST VINCENTS HOSP,INST HEART LUNG VASC,SYDNEY,NSW 2010,AUSTRALIA
[3] UNIV SYDNEY,MED,SYDNEY,NSW 2006,AUSTRALIA
来源
AUSTRALIAN AND NEW ZEALAND JOURNAL OF MEDICINE | 1991年 / 21卷 / 04期
关键词
ARRHYTHMOGENIC RIGHT VENTRICULAR DYSPLASIA; REENTRY; AUTOMATICITY; CATECHOLAMINE-SENSITIVITY;
D O I
10.1111/j.1445-5994.1991.tb01352.x
中图分类号
R5 [内科学];
学科分类号
1002 ; 100201 ;
摘要
A 23-year-old man presented with recurrent exercise-induced ventricular tachycardia (VT), complicated by systemic embolisation. Catecholamine - sensitive VT was reproduced on exercise testing and programmed electrical stimulation, displaying features suggestive of enhanced automaticity as well as re-entry. Both 2D-echocardiography and gated heart pool scan showed localised dyskinetic bulging in the right ventricle. A diagnosis of arrhythmogenic right ventricular dysplasia was made. This condition should be excluded in all young patients with otherwise unexplained ventricular arrhythmias.
引用
收藏
页码:451 / 453
页数:3
相关论文
共 9 条
[1]  
FONTAINE G, 1976, REENTRANT ARRHYTHMIA, P345
[2]  
GRIGG LE, 1985, AUST NZ J MED, V15, P634
[3]   HISTOLOGICAL DIAGNOSIS OF RIGHT VENTRICULAR DYSPLASIA - A ROLE FOR ELECTRON-MICROSCOPY [J].
GUIRAUDON, CM .
EUROPEAN HEART JOURNAL, 1989, 10 :95-96
[4]   CHARACTERISTICS, PROGNOSIS AND TREATMENT OF THE VENTRICULAR ARRHYTHMIAS OF RIGHT VENTRICULAR DYSPLASIA [J].
LECLERCQ, JF ;
COUMEL, P .
EUROPEAN HEART JOURNAL, 1989, 10 :61-67
[5]   NONISCHEMIC SUSTAINED VENTRICULAR-TACHYCARDIA - CLINICAL OUTCOME IN 12 PATIENTS WITH ARRHYTHMOGENIC RIGHT VENTRICULAR DYSPLASIA [J].
LEMERY, R ;
BRUGADA, P ;
JANSSEN, J ;
CHERIEX, E ;
DUGERNIER, T ;
WELLENS, HJJ .
JOURNAL OF THE AMERICAN COLLEGE OF CARDIOLOGY, 1989, 14 (01) :96-105
[6]   RIGHT VENTRICULAR DYSPLASIA - A REPORT OF 24 ADULT CASES [J].
MARCUS, FI ;
FONTAINE, GH ;
GUIRAUDON, G ;
FRANK, R ;
LAURENCEAU, JL ;
MALERGUE, C ;
GROSGOGEAT, Y .
CIRCULATION, 1982, 65 (02) :384-398
[7]   LEFT-VENTRICULAR INVOLVEMENT IN RIGHT VENTRICULAR CARDIOMYOPATHY [J].
PINAMONTI, B ;
SALVI, A ;
SILVESTRI, F ;
SINAGRA, G ;
CAMERINI, F .
EUROPEAN HEART JOURNAL, 1989, 10 :20-21
[8]   ELECTROPHYSIOLOGIC MECHANISM OF EXERCISE-INDUCED SUSTAINED VENTRICULAR-TACHYCARDIA [J].
SUNG, RJ ;
SHEN, EN ;
MORADY, F ;
SCHEINMAN, MM ;
HESS, D ;
BOTVINICK, EH .
AMERICAN JOURNAL OF CARDIOLOGY, 1983, 51 (03) :525-530
[9]  
VILLAIN E, 1990, ARCH MAL COEUR VAISS, V83, P665